117 results on '"Bos, Johan M."'
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2. Abstract 17329: Histone Modifications Regulate Hypertrophy Pathways in Obstructive Hypertrophic Cardiomyopathy
3. Abstract 15291: Early Outcomes With Left Cardiac Sympathetic Denervation for Medically Refractory Idiopathic Ventricular Fibrillation
4. Abstract 15229: An Artificial Intelligence Deep Neural Network Analysis of the 12-lead Electrocardiogram Distinguishes Patients With Congenital Long Qt Syndrome From Patients With Acquired Qt Prolongation
5. Abstract 15101: Return-to-Work for Patients in High-Risk Professions Diagnosed With a Sudden Death-Predisposing Genetic Heart Disease
6. Abstract 15058: Critical Reappraisal of Genetic Variants in Hypertrophic Cardiomyopathy
7. Abstract 13568: Characterization of the Maladaptive QTc Response During the Treadmill Exercise Test in Untreated Patients With Long QT Syndrome
8. Abstract 13153: Proteomic Differences in Sarcomere Positive HCM May Explain More Severe Clinical Differences
9. Abstract 12808: Genetic Heart Disease and Gender-Affirming Hormone Therapy in Transgender Individuals: Potential Pro-Arrhythmic Considerations
10. Abstract 12083: Highly Caffeinated Energy Drinks and Genetic Heart Disease-Associated Sudden Cardiac Arrest
11. Abstract 12069: Spectrum and Prevalence of Attention Deficit Hyperactivity Disorder (ADHD) and Intentional ADHD-Directed Pharmacotherapy in Patients With Catecholaminergic Polymorphic Ventricular Tachycardia
12. Vigorous Exercise in Patients With Congenital Long QT Syndrome: Results of the Prospective, Observational, Multinational LIVE-LQTS Study.
13. Flecainide Is Associated With a Lower Incidence of Arrhythmic Events in a Large Cohort of Patients With Catecholaminergic Polymorphic Ventricular Tachycardia
14. PO-04-202 RESUSCITATED OUT OF HOSPITAL CARDIAC ARREST AS THE INITIAL PRESENTATION OF HYPERTROPHIC CARDIOMYOPATHY
15. BS-452759-1 SPATIAL CLUSTERING ANALYSIS HIGHLIGHTS DISEASE-SPECIFIC 3-DIMENSIONAL DISTRIBUTION OF PATHOGENIC VARIANTS IN THE -ENCODED NAV1.5 CARDIAC SODIUM CHANNEL
16. EN-452414-5 VENTRICULAR CONDUCTION IS A MARKER FOR ARRHYTHMIC RISK IN OVERLAP SODIUM CHANNEL DISEASE
17. PO-03-231 BREAKTHROUGH CARDIAC EVENT RATE OF INITIALLY ASYMPTOMATIC LQTS PATIENTS
18. PO-02-142 MIRNA DOWN-REGULATE HYPERTROPHY AND INFLAMMATORY PATHWAYS IN THE TRANSCRIPTOME OF HYPERTROPHIC CARDIOMYOPATHY MYECTOMY TISSUE
19. PO-01-134 AN INTERNATIONAL MULTICENTER COHORT STUDY ON BETA-BLOCKER FREE TREATMENT STRATEGIES FOR CATECHOLAMINERGIC POLYMORPHIC VENTRICULAR TACHYCARDIA
20. PO-03-156 SPECTRUM AND PREVALENCE OF RYR2-OPATHIES DURING LIFE AND AFTER SUDDEN DEATH
21. PO-04-105 ELUCIDATION OF THE PREVALENCE, SPECTRUM, AND OUTCOMES IN PATIENTS WITH NON-PENETRANT LONG QT SYNDROME
22. PO-04-159 PREVALENCE AND CHARACTERISTICS OF PATIENTS WITH LONG QT SYNDROME (LQTS) WHO APPEAR NON-RESPONSIVE TO CONVENTIONAL LQTS THERAPIES
23. Abstract 16760: Frequency and Spectrum of Treatment Associated Side Effects and Complications in Patients With Long QT Syndrome
24. Abstract 16736: Risk Stratification With Treadmill Exercise Stress Testing in Patients With Long QT Syndrome
25. Biventricular Involvement In Hypertrophic Cardiomyopathy: Preliminary Analysis Of Cardiac MRIs With Visual Right Ventricular Hypertrophy
26. LB-469807-01 IMPACT OF VIGOROUS EXERCISE IN THE LONG QT SYNDROME BY GENOTYPE, AGE, AND SEX: DATA FROM THE LIFESTYLE AND EXERCISE IN LONG QT SYNDROME REGISTRY (LIVE-LQTS)
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29. Deep Unsupervised Clustering of Sparse Echo Data to Identify Patients for Implantation of Cardioverter-Defibrillator
30. An International Multi-Center Cohort Study on ß-blockers for the Treatment of Symptomatic Children with Catecholaminergic Polymorphic Ventricular Tachycardia
31. PO-04-001 OUTCOMES OF PATIENTS SUBSEQUENTLY DIAGNOSED WITH CONGENITAL LONG QT SYNDROME AFTER PRESENTING WITH A SENTINEL EVENT OF SUDDEN CARDIAC ARREST
32. PO-02-087 NEW IDENTIFIER OF ARRHYTHMIA RISK IN PATIENTS WITH CONGENITAL LONG-QT SYNDROME
33. PO-02-089 AN EXAMINATION OF GUIDELINE-DIRECTED DEVICE THERAPY WITH AN IMPLANTABLE CARDIOVERTER-DEFIBRILLATOR FOR LONG QT SYNDROME
34. PO-02-090 IMPLANTABLE CARDIOVERTER DEFIBRILLATOR THERAPY FOR CHANNELOPATHIES: A SINGLE CENTER EXPERIENCE
35. PO-01-040 TRIGGER TYPE AND SUBSEQUENT BREAKTHROUGH CARDIAC EVENTS IN PATIENTS WITH EITHER LONG QT SYNDROME OR CATECHOLAMINERGIC POLYMORPHIC VENTRICULAR TACHYCARDIA AFTER LEFT CARDIAC SYMPATHETIC DENERVATION
36. PO-01-188 A MULTI-OMIC COMPARISON OF SURGICAL MYECTOMY LEFT VENTRICULAR TISSUE REVEALS SEX-SPECIFIC DIFFERENCES IN OBSTRUCTIVE HYPERTROPHIC CARDIOMYOPATHY
37. MP-470544-005 DEFINING THE PREVALENCE AND PHENOTYPE OF CHILDREN WITH BRUGADA SYNDROME WHO ARE NON-RESPONDERS TO CONVENTIONAL BRUGADA SYNDROME-DIRECTED THERAPIES
38. MP-470544-001 LEFT CARDIAC SYMPATHETIC DENERVATION AS ADJUVANT TREATMENT FOR THE PREVENTION OF CHANNELOPATHY-MEDIATED MALIGNANT ARRHYTHMIAS IN CHILDREN: EXPERIENCE FROM TWO REFERRAL CENTERS
39. BS-469619-003 GRANULAR VARIANT-SPECIFIC FEATURES IMPROVE KCNH2-LONG QT SYNDROME RISK STRATIFICATION
40. CE-482905-003 EFFICACY OF MEXILETINE FOR LQT2: EVIDENCE FROM HIPSC-DERIVED CARDIOMYOCYTES, TRANSGENIC RABBITS AND PATIENTS
41. CE-482906-004 OUTCOMES AND BURDENS TO RETURN TO PLAY FOR PHENOTYPE NEGATIVE ATHLETES WITH A GENETIC HEART DISEASE-ASSOCIATED POSITIVE GENETIC TEST
42. An International Multicenter Cohort Study on β-Blockers for the Treatment of Symptomatic Children With Catecholaminergic Polymorphic Ventricular Tachycardia
43. Abstract 11386: Self-Service Analysis of Best Practice Alert Acknowledgement Comments as a Method for Evaluation Reveals Opportunities for Optimization of Clinical Decision Support for Patients with Prolonged QT Syndrome
44. PO-03-143 PREVALENCE AND CLINICAL COURSE OF PEDIATRIC-ONSET ARRHYTHMOGENIC CARDIOMYOPATHY
45. BS-452759-1 SPATIAL CLUSTERING ANALYSIS HIGHLIGHTS DISEASE-SPECIFIC 3-DIMENSIONAL DISTRIBUTION OF PATHOGENIC VARIANTS IN THE SCN5A-ENCODED NAV1.5 CARDIAC SODIUM CHANNEL
46. Molecular basis for clinical heterogeneity in inherited cardiomyopathies due to myopalladin mutations
47. Prevalence and clinical phenotype of concomitant long QT syndrome and arrhythmogenic bileaflet mitral valve prolapse
48. Sleep Disordered Breathing in Hypertrophic Cardiomyopathy
49. Sleep Disordered Breathing in Hypertrophic Cardiomyopathy.
50. SCN5A mutations in 442 neonates and children: genotype–phenotype correlation and identification of higher-risk subgroups
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