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1,211 results on '"Aghamohammadi, Asghar"'

2. International retrospective study of allogeneic hematopoietic cell transplantation for activated PI3K-delta syndrome.

Author

Dimitrova, Dimana, Nademi, Zohreh, Maccari, Maria Elena, Ehl, Stephan, Uzel, Gulbu, Tomoda, Takahiro, Okano, Tsubasa, Imai, Kohsuke, Carpenter, Benjamin, Ip, Winnie, Rao, Kanchan, Worth, Austen JJ, Laberko, Alexandra, Mukhina, Anna, Néven, Bénédicte, Moshous, Despina, Speckmann, Carsten, Warnatz, Klaus, Wehr, Claudia, Abolhassani, Hassan, Aghamohammadi, Asghar, Bleesing, Jacob J, Dara, Jasmeen, Dvorak, Christopher C, Ghosh, Sujal, Kang, Hyoung Jin, Markelj, Gašper, Modi, Arunkumar, Bayer, Diana K, Notarangelo, Luigi D, Schulz, Ansgar, Garcia-Prat, Marina, Soler-Palacín, Pere, Karakükcü, Musa, Yilmaz, Ebru, Gambineri, Eleonora, Menconi, Mariacristina, Masmas, Tania N, Holm, Mette, Bonfim, Carmem, Prando, Carolina, Hughes, Stephen, Jolles, Stephen, Morris, Emma C, Kapoor, Neena, Koltan, Sylwia, Paneesha, Shankara, Steward, Colin, Wynn, Robert, Duffner, Ulrich, Gennery, Andrew R, Lankester, Arjan C, Slatter, Mary, and Kanakry, Jennifer A

Subjects
Humans, Treatment Outcome, Hematopoietic Stem Cell Transplantation, Transplantation, Homologous, Retrospective Studies, Graft Rejection, Adolescent, Adult, Aged, Middle Aged, Child, Child, Preschool, Female, Male, Young Adult, Phosphatidylinositol 3-Kinases, Kaplan-Meier Estimate, Class I Phosphatidylinositol 3-Kinases, Primary Immunodeficiency Diseases, MTOR Inhibitors, Primary immunodeficiency, activated phosphoinositide 3-kinase delta syndrome, allogeneic hematopoietic cell transplantation, graft failure, lymphoproliferation, mTOR inhibitor, serotherapy, Rare Diseases, Cancer, Transplantation, Regenerative Medicine, Hematology, allogeneic hemato-poietic cell transplantation, Immunology, Allergy
Abstract

BackgroundActivated phosphoinositide 3-kinase delta syndrome (APDS) is a combined immunodeficiency with a heterogeneous phenotype considered reversible by allogeneic hematopoietic cell transplantation (HCT).ObjectivesThis study sought to characterize HCT outcomes in APDS.MethodsRetrospective data were collected on 57 patients with APDS1/2 (median age, 13 years; range, 2-66 years) who underwent HCT.ResultsPre-HCT comorbidities such as lung, gastrointestinal, and liver pathology were common, with hematologic malignancy in 26%. With median follow-up of 2.3 years, 2-year overall and graft failure-free survival probabilities were 86% and 68%, respectively, and did not differ significantly by APDS1 versus APDS2, donor type, or conditioning intensity. The 2-year cumulative incidence of graft failure following first HCT was 17% overall but 42% if mammalian target of rapamycin inhibitor(s) (mTORi) were used in the first year post-HCT, compared with 9% without mTORi. Similarly, 2-year cumulative incidence of unplanned donor cell infusion was overall 28%, but 65% in the context of mTORi receipt and 23% without. Phenotype reversal occurred in 96% of evaluable patients, of whom 17% had mixed chimerism. Vulnerability to renal complications continued post-HCT, adding new insights into potential nonimmunologic roles of phosphoinositide 3-kinase not correctable through HCT.ConclusionsGraft failure, graft instability, and poor graft function requiring unplanned donor cell infusion were major barriers to successful HCT. Post-HCT mTORi use may confer an advantage to residual host cells, promoting graft instability. Longer-term post-HCT follow-up of more patients is needed to elucidate the kinetics of immune reconstitution and donor chimerism, establish approaches that reduce graft instability, and assess the completeness of phenotype reversal over time.

Published
2022

3. The urgent need for integrated science to fight COVID-19 pandemic and beyond

Author

Moradian, Negar, Ochs, Hans D, Sedikies, Constantine, Hamblin, Michael R, Camargo, Carlos A, Martinez, J Alfredo, Biamonte, Jacob D, Abdollahi, Mohammad, Torres, Pedro J, Nieto, Juan J, Ogino, Shuji, Seymour, John F, Abraham, Ajith, Cauda, Valentina, Gupta, Sudhir, Ramakrishna, Seeram, Sellke, Frank W, Sorooshian, Armin, Wallace Hayes, A, Martinez-Urbistondo, Maria, Gupta, Manoj, Azadbakht, Leila, Esmaillzadeh, Ahmad, Kelishadi, Roya, Esteghamati, Alireza, Emam-Djomeh, Zahra, Majdzadeh, Reza, Palit, Partha, Badali, Hamid, Rao, Idupulapati, Saboury, Ali Akbar, Jagan Mohan Rao, L, Ahmadieh, Hamid, Montazeri, Ali, Fadini, Gian Paolo, Pauly, Daniel, Thomas, Sabu, Moosavi-Movahed, Ali A, Aghamohammadi, Asghar, Behmanesh, Mehrdad, Rahimi-Movaghar, Vafa, Ghavami, Saeid, Mehran, Roxana, Uddin, Lucina Q, Von Herrath, Matthias, Mobasher, Bahram, and Rezaei, Nima

Subjects
Biomedical and Clinical Sciences, Health Sciences, Infection, Good Health and Well Being, Betacoronavirus, Biomedical Research, COVID-19, Coronavirus Infections, Delivery of Health Care, Integrated, Emergencies, Health Services Needs and Demand, History, 21st Century, Humans, Interdisciplinary Communication, Interdisciplinary Studies, Pandemics, Pneumonia, Viral, Public Health, SARS-CoV-2, Coronavirus, Complex problems, Collaboration, Interdisciplinarity, Public health, Medical and Health Sciences, Immunology, Biomedical and clinical sciences, Health sciences
Abstract

The COVID-19 pandemic has become the leading societal concern. The pandemic has shown that the public health concern is not only a medical problem, but also affects society as a whole; so, it has also become the leading scientific concern. We discuss in this treatise the importance of bringing the world's scientists together to find effective solutions for controlling the pandemic. By applying novel research frameworks, interdisciplinary collaboration promises to manage the pandemic's consequences and prevent recurrences of similar pandemics.

Published
2020

4. The urgent need for integrated science to fight COVID-19 pandemic and beyond.

Author

Ramakrishna, Seeram, Sellke, Frank, Sorooshian, Armin, Wallace Hayes, A, Martinez-Urbistondo, Maria, Gupta, Manoj, Azadbakht, Leila, Esmaillzadeh, Ahmad, Kelishadi, Roya, Esteghamati, Alireza, Emam-Djomeh, Zahra, Majdzadeh, Reza, Palit, Partha, Badali, Hamid, Rao, Idupulapati, Saboury, Ali, Jagan Mohan Rao, L, Ahmadieh, Hamid, Montazeri, Ali, Fadini, Gian, Pauly, Daniel, Thomas, Sabu, Moosavi-Movahed, Ali, Aghamohammadi, Asghar, Behmanesh, Mehrdad, Rahimi-Movaghar, Vafa, Ghavami, Saeid, Mehran, Roxana, Uddin, Lucina, Von Herrath, Matthias, Mobasher, Bahram, Rezaei, Nima, Moradian, Negar, Ochs, Hans, Sedikies, Constantine, Hamblin, Michael, Camargo, Carlos, Martinez, J, Biamonte, Jacob, Abdollahi, Mohammad, Torres, Pedro, Nieto, Juan, Ogino, Shuji, Seymour, John, Abraham, Ajith, Cauda, Valentina, and Gupta, Sudhir

Subjects
COVID-19, Collaboration, Complex problems, Coronavirus, Interdisciplinarity, Public health, Betacoronavirus, Biomedical Research, COVID-19, Coronavirus Infections, Delivery of Health Care, Integrated, Emergencies, Health Services Needs and Demand, History, 21st Century, Humans, Interdisciplinary Communication, Interdisciplinary Studies, Pandemics, Pneumonia, Viral, Public Health, SARS-CoV-2
Abstract

The COVID-19 pandemic has become the leading societal concern. The pandemic has shown that the public health concern is not only a medical problem, but also affects society as a whole; so, it has also become the leading scientific concern. We discuss in this treatise the importance of bringing the worlds scientists together to find effective solutions for controlling the pandemic. By applying novel research frameworks, interdisciplinary collaboration promises to manage the pandemics consequences and prevent recurrences of similar pandemics.

Published
2020

5. Disease Progression of WHIM Syndrome in an International Cohort of 66 Pediatric and Adult Patients

Author

Geier, Christoph B., Ellison, Maryssa, Cruz, Rachel, Pawar, Sumit, Leiss-Piller, Alexander, Zmajkovicova, Katarina, McNulty, Shannon M, Yilmaz, Melis, Evans, 2nd, Martin Oman, Gordon, Sumai, Ujhazi, Boglarka, Wiest, Ivana, Abolhassani, Hassan, Aghamohammadi, Asghar, Barmettler, Sara, Bhar, Saleh, Bondarenko, Anastasia, Bolyard, Audrey Anna, Buchbinder, David, Cada, Michaela, Cavieres, Mirta, Connelly, James A., Dale, David C., Deordieva, Ekaterina, Dorsey, Morna J., Drysdale, Simon B., Ehl, Stephan, Elfeky, Reem, Fioredda, Francesca, Firkin, Frank, Förster-Waldl, Elizabeth, Geng, Bob, Goda, Vera, Gonzalez-Granado, Luis, Grunebaum, Eyal, Grzesk, Elzbieta, Henrickson, Sarah E., Hilfanova, Anna, Hiwatari, Mitsuteru, Imai, Chihaya, Ip, Winnie, Jyonouchi, Soma, Kanegane, Hirokazu, Kawahara, Yuta, Khojah, Amer M., Kim, Vy Hong-Diep, Kojić, Marina, Kołtan, Sylwia, Krivan, Gergely, Langguth, Daman, Lau, Yu-Lung, Leung, Daniel, Miano, Maurizio, Mersyanova, Irina, Mousallem, Talal, Muskat, Mica, Naoum, Flavio A., Noronha, Suzie A., Ouederni, Monia, Ozono, Shuichi, Richmond, G. Wendell, Sakovich, Inga, Salzer, Ulrich, Schuetz, Catharina, Seeborg, Filiz Odabasi, Sharapova, Svetlana O., Sockel, Katja, Volokha, Alla, von Bonin, Malte, Warnatz, Klaus, Wegehaupt, Oliver, Weinberg, Geoffrey A., Wong, Ke-Juin, Worth, Austen, Yu, Huang, Zharankova, Yulia, Zhao, Xiaodong, Devlin, Lisa, Badarau, Adriana, Csomos, Krisztian, Keszei, Marton, Pereira, Joao, Taveras, Arthur G, Beaussant-Cohen, Sarah L., Ong, Mei-Sing, Shcherbina, Anna, and Walter, Jolan E.

Published
2022
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6. Outcomes and Treatment Strategies for Autoimmunity and Hyperinflammation in Patients with RAG Deficiency

Author

Farmer, Jocelyn R, Foldvari, Zsofia, Ujhazi, Boglarka, De Ravin, Suk See, Chen, Karin, Bleesing, Jack JH, Schuetz, Catharina, Al-Herz, Waleed, Abraham, Roshini S, Joshi, Avni Y, Costa-Carvalho, Beatriz T, Buchbinder, David, Booth, Claire, Reiff, Andreas, Ferguson, Polly J, Aghamohammadi, Asghar, Abolhassani, Hassan, Puck, Jennifer M, Adeli, Mehdi, Cancrini, Caterina, Palma, Paolo, Bertaina, Alice, Locatelli, Franco, Di Matteo, Gigliola, Geha, Raif S, Kanariou, Maria G, Lycopoulou, Lilia, Tzanoudaki, Marianna, Sleasman, John W, Parikh, Suhag, Pinero, Gloria, Fischer, Bernard M, Dbaibo, Ghassan, Unal, Ekrem, Patiroglu, Turkan, Karakukcu, Musa, Al-Saad, Khulood Khalifa, Dilley, Meredith A, Pai, Sung-Yun, Dutmer, Cullen M, Gelfand, Erwin W, Geier, Christoph B, Eibl, Martha M, Wolf, Hermann M, Henderson, Lauren A, Hazen, Melissa M, Bonfim, Carmem, Wolska-Kuśnierz, Beata, Butte, Manish J, Hernandez, Joseph D, Nicholas, Sarah K, Stepensky, Polina, Chandrakasan, Shanmuganathan, Miano, Maurizio, Westermann-Clark, Emma, Goda, Vera, Kriván, Gergely, Holland, Steven M, Fadugba, Olajumoke, Henrickson, Sarah E, Ozen, Ahmet, Karakoc-Aydiner, Elif, Baris, Safa, Kiykim, Ayca, Bredius, Robbert, Hoeger, Birgit, Boztug, Kaan, Pashchenko, Olga, Neven, Benedicte, Moshous, Despina, Villartay, Jean-Pierre de, Bousfiha, Ahmed Aziz, Hill, Harry R, Notarangelo, Luigi D, and Walter, Jolan E

Subjects
Autoimmune Disease, Genetics, Hematology, Inflammatory and immune system, Adolescent, Adult, Autoimmunity, Child, Child, Preschool, Female, Hematopoietic Stem Cell Transplantation, Homeodomain Proteins, Humans, Immunologic Deficiency Syndromes, Immunosuppressive Agents, Infant, Inflammation, Male, Middle Aged, Treatment Outcome, Young Adult, Recombination activating gene, Severe combined immunodeficiency, Immune dysregulation, Autoimmune cytopenias, Hematopoietic stem cell transplantation
Abstract

BACKGROUND:Although autoimmunity and hyperinflammation secondary to recombination activating gene (RAG) deficiency have been associated with delayed diagnosis and even death, our current understanding is limited primarily to small case series. OBJECTIVE:Understand the frequency, severity, and treatment responsiveness of autoimmunity and hyperinflammation in RAG deficiency. METHODS:In reviewing the literature and our own database, we identified 85 patients with RAG deficiency, reported between 2001 and 2016, and compiled the largest case series to date of 63 patients with prominent autoimmune and/or hyperinflammatory pathology. RESULTS:Diagnosis of RAG deficiency was delayed a median of 5 years from the first clinical signs of immune dysregulation. Most patients (55.6%) presented with more than 1 autoimmune or hyperinflammatory complication, with the most common etiologies being cytopenias (84.1%), granulomas (23.8%), and inflammatory skin disorders (19.0%). Infections, including live viral vaccinations, closely preceded the onset of autoimmunity in 28.6% of cases. Autoimmune cytopenias had early onset (median, 1.9, 2.1, and 2.6 years for autoimmune hemolytic anemia, immune thrombocytopenia, and autoimmune neutropenia, respectively) and were refractory to intravenous immunoglobulin, steroids, and rituximab in most cases (64.7%, 73.7%, and 71.4% for autoimmune hemolytic anemia, immune thrombocytopenia, and autoimmune neutropenia, respectively). Evans syndrome specifically was associated with lack of response to first-line therapy. Treatment-refractory autoimmunity/hyperinflammation prompted hematopoietic stem cell transplantation in 20 patients. CONCLUSIONS:Autoimmunity/hyperinflammation can be a presenting sign of RAG deficiency and should prompt further evaluation. Multilineage cytopenias are often refractory to immunosuppressive treatment and may require hematopoietic cell transplantation for definitive management.

Published
2019

11. Initial presenting manifestations in 16,486 patients with inborn errors of immunity include infections and noninfectious manifestations

Author

Boztug, Kaan, Brunner, Juergen, Demel, Ulrike F., Förster-Waldl, Elisabeth, Gasteiger, Lukas M., Göschl, Lisa, Kojić, Marina, Schroll, Andrea, Seidel, Markus G., Wintergerst, Uwe, Wisgrill, Lukas, Sharapova, Svetlana O., Goffard, Jean-Christophe, Kerre, Tessa, Meyts, Isabelle, Roosens, Fine, Smet, Julie, Haerynck, Filomeen, Eric, Zelimir Pavle, Milenova, Veneta, Gagro, Alenka, Richter, Darko, Chovancova, Zita, Hlavackova, Eva, Litzman, Jiri, Milota, Tomas, Sediva, Anna, Elaziz, Dalia Abd, Alkady, Radwa Salaheldin, El Sayed El Hawary, Rabab, Eldash, Alia S., Galal, Nermeen, Lotfy, Sohilla, Meshaal, Safa S., Reda, Shereen M., Sobh, Ali, Elmarsafy, Aisha, Seppänen, Mikko R.J., Brosselin, Pauline, Courteille, Virginie, De Vergnes, Nathalie, Kracker, Sven, Pergent, Martine, Randrianomenjanahary, Philippe, Ahrenstorf, Gerrit, Albert, Michael H., Ankermann, Tobias, Atschekzei, Faranaz, Baumann, Ulrich, Becker, Benjamin C., Behrends, Uta, Belohradsky, Bernd H., Biegner, Anika-Kerstin, Binder, Nadine, Bode, Sebastian F.N., Boesecke, Christoph, Boetticher, Benedikt, Borte, Michael, Borte, Stephan, Classen, Carl Friedrich, Dirks, Johannes, Dückers, Gregor, El-Helou, Sabine, Ernst, Diana, Fasshauer, Maria, Fecker, Gisela, Felgentreff, Kerstin, Foell, Dirk, Ghosh, Sujal, Girschick, Hermann J., Goldacker, Sigune, Graf, Norbert, Graf, Dagmar, Greil, Johann, Hanitsch, Leif Gunnar, Hauck, Fabian, Heeg, Maximilian, Heine, Sabine I., Henes, Joerg C., Hoenig, Manfred, Holzer, Ursula, Holzinger, Dirk, Horneff, Gerd, Hundsdoerfer, Patrick, Jablonka, Alexandra, Jakoby, Donate, Joean, Oana, Kaiser-Labusch, Petra, Klemann, Christian, Kobbe, Robin, Körholz, Julia, Kramm, Christof M., Krüger, Renate, Landwehr-Kenzel, Sybille, Lehmberg, Kai, Liese, Johannes G., Lippert, Conrad Ferdinand, Maccari, Maria Elena, Masjosthusmann, Katja, Meinhardt, Andrea, Metzler, Markus, Morbach, Henner, Müller, Ingo, Naumann-Bartsch, Nora, Neubert, Jennifer, Niehues, Tim, Peter, Hans-Hartmut, Rieber, Nikolaus, Ritterbusch, Henrike, Rockstroh, Jürgen Kurt, Roesler, Joachim, Schauer, Uwe, Scheible, Raphael, Schmalzing, Marc, Schmidt, Reinhold Ernst, Schneider, Dominik T., Schreiber, Stefan, Schuetz, Catharina, Schulz, Ansgar, Schulze-Koops, Hendrik, Schulze-Sturm, Ulf, Schuster, Volker, Schwaneck, Eva C., Schwarz, Klaus, Schwarze-Zander, Carolynne, Sirin, Mehtap, Skapenko, Alla, Sogkas, Georgios, Sparber-Sauer, Monika, Speckmann, Carsten, Steinmann, Sandra, Stiehler, Sophie, Tenbrock, Klaus, von Bernuth, Horst, Warnatz, Klaus, Wasmuth, Jan-Christian, Weiss, Michael, Witte, Torsten, Wittke, Kirsten, Wittkowski, Helmut, Zeuner, Rainald A., Farmaki, Evangelia, Hatzistilianou, Maria N., Kakkas, Ioannis, Kanariou, Maria G., Kapousouzi, Androniki, Liatsis, Emmanouil, Maggina, Paraskevi, Papadopoulou-Alataki, Efimia, Raptaki, Maria, Speletas, Matthaios, Tantou, Sofia, Goda, Vera, Kriván, Gergely, Marodi, Laszlo, Abolhassani, Hassan, Aghamohammadi, Asghar, Rezaei, Nima, Feighery, Conleth, Leahy, Timothy Ronan, Ryan, Paul, Batzir, Nurit Assia, Garty, Ben Zion, Tamary, Hannah, Aiuti, Alessandro, Amodio, Donato, Azzari, Chiara, Barzaghi, Federica, Baselli, Lucia A., Cancrini, Caterina, Carrabba, Maria, Cazzaniga, Marco, Cesaro, Simone, Chinello, Matteo, Danieli, Maria Giovanna, Dellepiane, Rosa Maria, Fabio, Giovanna, Gambineri, Eleonora, Lodi, Lorenzo, Lougaris, Vassilios, Marasco, Carolina, Martire, Baldassarre, Marzollo, Antonio, Milito, Cinzia, Moschese, Viviana, Pignata, Claudio, Plebani, Alessandro, Porta, Fulvio, Quinti, Isabella, Ricci, Silvia, Soresina, Annarosa, Tommasini, Alberto, Vacca, Angelo, Vanessa, Clementina, Blažienė, Audra, Sitkauskiene, Brigita, Gowin, Ewelina, Heropolitańska-Pliszka, Edyta, Pietrucha, Barbara, Szaflarska, Anna, Więsik-Szewczyk, Ewa, Wolska-Kuśnierz, Beata, Esteves, Isabel, Faria, Emilia, Marques, Laura Hora, Neves, João Farela, Silva, Susana L., Teixeira, Carla, Pereira da Silva, Sara, Capilna, Brindusa Ruxandra, Guseva, Marina N., Shcherbina, Anna, Bobcakova, Anna, Ciznar, Peter, Gabzdilova, Juliana, Jesenak, Milos, Kapustova, Lenka, Orosova, Jaroslava, Petrovicova, Otilia, Raffac, Stefan, Kopač, Peter, Allende, Luis M., Antolí, Arnau, Blanch, Gemma Rocamora, Carbone, Javier, Dieli-Crimi, Romina, Garcia-Prat, Marina, Gil-Herrera, Juana, Gonzalez-Granado, Luis Ignacio, Agulló, Pilar Llobet, Olbrich, Peter, Parra-Martínez, Alba, Paz-Artal, Estela, Pleguezuelo, Daniel E., Rodríguez, Nerea Salmón, Sánchez-Ramón, Silvia, Santos-Pérez, Juan Luis, Solanich, Xavier, Soler-Palacin, Pere, González-Amores, Miriam, Ekwall, Olov, Fasth, Anders, Bitzenhofer-Grüber, Michaela, Candotti, Fabio, Dimitriou, Florentia, Heininger, Ulrich, Holbro, Andreas, Jandus, Peter, Kolios, Antonios G.A., Marschall, Karin, Schmid, Jana Pachlopnik, Posfay-Barbe, Klara M., Prader, Seraina, Reichenbach, Janine, Steiner, Urs C., Trück, Johannes, Bredius, Robbert G., de Kruijf- Bazen, Suzanne, de Vries, Esther, Henriet, Stefanie S.V., Kuijpers, Taco W., Potjewijd, Judith, Rutgers, Abraham, Stol, Kim, van Aerde, Koen J., Van den Berg, J. Merlijn, van de Ven, Annick A.J.M., Montfrans, Jorisvan, Aydemir, Sezin, Baris, Safa, Dogu, Figen, Ikinciogullari, Aydan, Karakoc-Aydiner, Elif, Kilic, Sara S., Kiykim, Ayca, Kökçü Karadağ, Şefika İlknur, Kutukculer, Necil, Ocak, Suheyla, UNAL, Ekrem, Boyarchuk, Oksana, Hilfanova, Anna, Kostyuchenko, Larysa V., Alachkar, Hana, Arkwright, Peter D., Baxendale, Helen E., Bernatoniene, Jolanta, Coulter, Tanya I., Garcez, Tomaz, Goddard, Sarah, Gompels, Mark M., Grigoriadou, Sofia, Herriot, Richard, Herwadkar, Archana, Huissoon, Aarnoud, Ibberson, Lisa, Nademi, Zoreh, Noorani, Sadia, Parvin, Shahnaz, Steele, Cathal Laurence, Thomas, Moira, Waruiru, Catherine, Yong, Patrick F.K., Bourne, Helen, Thalhammer, Julian, Kindle, Gerhard, Nieters, Alexandra, Rusch, Stephan, Fischer, Alain, Grimbacher, Bodo, Edgar, David, Buckland, Matthew, Mahlaoui, Nizar, and Ehl, Stephan

Published
2021
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12. Adverse reactions in a large cohort of patients with inborn errors of immunity receiving intravenous immunoglobulin

Author

Esmaeilzadeh, Hossein, Askarisarvestani, Aida, Hosseini, Nazanin, Samimi, Sahar, Shafiei, Alireza, Mahdaviani, Seyed Alireza, Eslami, Narges, Chavoshzadeh, Zahra, Fallahi, Mazdak, Khakbazanfard, Nasrin, Shabestari, Mahnaz Sadeghi, Aleyasin, Soheila, Nabavizadeh, Seyed Hesamedin, Cheraghi, Taher, Kalantari, Arash, Ahmadiafshar, Akefeh, Safari, Mojgan, Eslamian, Mohammad Hossein, Molatefi, Rasol, Shirkani, Afshin, Heidarzadeh Arani, Marzieh, Tavakol, Marzieh, Bemanian, Mohammad Hassan, Arshi, Saba, Nabavi, Mohammad, Shokri, Sima, Shahhosseini, Babak, Mortazavi, Negar, Nakhaei, Pooria, Nazari, Farzad, Fallahpour, Morteza, Ahanchian, Hamid, Moazzen, Nasrin, Khoshkhui, Maryam, Motlagh, Ahmad Vosughi, Aghamohammadi, Asghar, Abolhassani, Hassan, Yazdani, Reza, and Rezaei, Nima

Published
2021
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13. Long-term outcomes of 176 patients with X-linked hyper-IgM syndrome treated with or without hematopoietic cell transplantation.

Author

de la Morena, M Teresa, Leonard, David, Torgerson, Troy R, Cabral-Marques, Otavio, Slatter, Mary, Aghamohammadi, Asghar, Chandra, Sharat, Murguia-Favela, Luis, Bonilla, Francisco A, Kanariou, Maria, Damrongwatanasuk, Rongras, Kuo, Caroline Y, Dvorak, Christopher C, Meyts, Isabelle, Chen, Karin, Kobrynski, Lisa, Kapoor, Neena, Richter, Darko, DiGiovanni, Daniela, Dhalla, Fatima, Farmaki, Evangelia, Speckmann, Carsten, Español, Teresa, Shcherbina, Anna, Hanson, Imelda Celine, Litzman, Jiri, Routes, John M, Wong, Melanie, Fuleihan, Ramsay, Seneviratne, Suranjith L, Small, Trudy N, Janda, Ales, Bezrodnik, Liliana, Seger, Reinhard, Raccio, Andrea Gomez, Edgar, J David M, Chou, Janet, Abbott, Jordan K, van Montfrans, Joris, González-Granado, Luis Ignacio, Bunin, Nancy, Kutukculer, Necil, Gray, Paul, Seminario, Gisela, Pasic, Srdjan, Aquino, Victor, Wysocki, Christian, Abolhassani, Hassan, Dorsey, Morna, Cunningham-Rundles, Charlotte, Knutsen, Alan P, Sleasman, John, Costa Carvalho, Beatriz Tavares, Condino-Neto, Antonio, Grunebaum, Eyal, Chapel, Helen, Ochs, Hans D, Filipovich, Alexandra, Cowan, Mort, Gennery, Andrew, Cant, Andrew, Notarangelo, Luigi D, and Roifman, Chaim M

Subjects
Humans, Hematopoietic Stem Cell Transplantation, Proportional Hazards Models, Retrospective Studies, Cohort Studies, Follow-Up Studies, Time, Adolescent, Adult, Middle Aged, Child, Child, Preschool, Infant, Female, Male, Hyper-IgM Immunodeficiency Syndrome, Young Adult, Kaplan-Meier Estimate, CD40 ligand, Karnofsky/Lansky scores, X-linked hyper-IgM syndrome, defects in class-switch recombination, hematopoietic cell transplantation, long-term outcomes, primary immunodeficiency, Pediatric, Clinical Research, Transplantation, Inflammatory and immune system, Good Health and Well Being, Immunology, Allergy
Abstract

BackgroundX-linked hyper-IgM syndrome (XHIGM) is a primary immunodeficiency with high morbidity and mortality compared with those seen in healthy subjects. Hematopoietic cell transplantation (HCT) has been considered a curative therapy, but the procedure has inherent complications and might not be available for all patients.ObjectivesWe sought to collect data on the clinical presentation, treatment, and follow-up of a large sample of patients with XHIGM to (1) compare long-term overall survival and general well-being of patients treated with or without HCT along with clinical factors associated with mortality and (2) summarize clinical practice and risk factors in the subgroup of patients treated with HCT.MethodsPhysicians caring for patients with primary immunodeficiency diseases were identified through the Jeffrey Modell Foundation, United States Immunodeficiency Network, Latin American Society for Immunodeficiency, and Primary Immune Deficiency Treatment Consortium. Data were collected with a Research Electronic Data Capture Web application. Survival from time of diagnosis or transplantation was estimated by using the Kaplan-Meier method compared with log-rank tests and modeled by using proportional hazards regression.ResultsTwenty-eight clinical sites provided data on 189 patients given a diagnosis of XHIGM between 1964 and 2013; 176 had valid follow-up and vital status information. Sixty-seven (38%) patients received HCT. The average follow-up time was 8.5 ± 7.2 years (range, 0.1-36.2 years). No difference in overall survival was observed between patients treated with or without HCT (P = .671). However, risk associated with HCT decreased for diagnosis years 1987-1995; the hazard ratio was significantly less than 1 for diagnosis years 1995-1999. Liver disease was a significant predictor of overall survival (hazard ratio, 4.9; 95% confidence limits, 2.2-10.8; P

Published
2017

14. Extended clinical and immunological phenotype and transplant outcome in CD27 and CD70 deficiency

Author

Ghosh, Sujal, Köstel Bal, Sevgi, Edwards, Emily S.J., Pillay, Bethany, Jiménez Heredia, Raúl, Erol Cipe, Funda, Rao, Geetha, Salzer, Elisabeth, Zoghi, Samaneh, Abolhassani, Hassan, Momen, Tooba, Gostick, Emma, Price, David A., Zhang, Yu, Oler, Andrew J., Gonzaga-Jauregui, Claudia, Erman, Baran, Metin, Ayse, Ilhan, Inci, Haskologlu, Sule, Islamoglu, Candan, Baskin, Kubra, Ceylaner, Serdar, Yilmaz, Ebru, Unal, Ekrem, Karakukcu, Musa, Berghuis, Dagmar, Cole, Theresa, Gupta, Aditya K., Hauck, Fabian, Kogler, Hubert, Hoepelman, Andy I.M., Baris, Safa, Karakoc-Aydiner, Elif, Ozen, Ahmet, Kager, Leo, Holzinger, Dirk, Paulussen, Michael, Krüger, Renate, Meisel, Roland, Oommen, Prasad T., Morris, Emma, Neven, Benedicte, Worth, Austen, van Montfrans, Joris, Fraaij, Pieter L.A., Choo, Sharon, Dogu, Figen, Davies, E. Graham, Burns, Siobhan, Dückers, Gregor, Becker, Ruy Perez, von Bernuth, Horst, Latour, Sylvain, Faraci, Maura, Gattorno, Marco, Su, Helen C., Pan-Hammarström, Qiang, Hammarström, Lennart, Lenardo, Michael J., Ma, Cindy S., Niehues, Tim, Aghamohammadi, Asghar, Rezaei, Nima, Ikinciogullari, Aydan, Tangye, Stuart G., Lankester, Arjan C., and Boztug, Kaan

Published
2020
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20. Long-term outcome of LRBA deficiency in 76 patients after various treatment modalities as evaluated by the immune deficiency and dysregulation activity (IDDA) score

Author

Tesch, Victoria Katharina, Abolhassani, Hassan, Shadur, Bella, Zobel, Joachim, Mareika, Yuliya, Sharapova, Svetlana, Karakoc-Aydiner, Elif, Rivière, Jacques G., Garcia-Prat, Marina, Moes, Nicolette, Haerynck, Filomeen, Gonzales-Granado, Luis I., Santos Pérez, Juan Luis, Mukhina, Anna, Shcherbina, Anna, Aghamohammadi, Asghar, Hammarström, Lennart, Dogu, Figen, Haskologlu, Sule, İkincioğulları, Aydan İ., Köstel Bal, Sevgi, Baris, Safa, Kilic, Sara Sebnem, Karaca, Neslihan Edeer, Kutukculer, Necil, Girschick, Hermann, Kolios, Antonios, Keles, Sevgi, Uygun, Vedat, Stepensky, Polina, Worth, Austen, van Montfrans, Joris M., Peters, Anke M.J., Meyts, Isabelle, Adeli, Mehdi, Marzollo, Antonio, Padem, Nurcicek, Khojah, Amer M., Chavoshzadeh, Zahra, Avbelj Stefanija, Magdalena, Bakhtiar, Shahrzad, Florkin, Benoit, Meeths, Marie, Gamez, Laura, Grimbacher, Bodo, Seppänen, Mikko R.J., Lankester, Arjan, Gennery, Andrew R., and Seidel, Markus G.

Published
2020
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24. Predominantly Antibody Deficiencies

Author

Aghamohammadi, Asghar, Plebani, Alessandro, Lougaris, Vassilios, Durandy, Anne, Condino-Neto, Antonio, Kanegane, Hirokazu, Hammarström, Lennart, Rezaei, Nima, editor, Aghamohammadi, Asghar, editor, and Notarangelo, Luigi D., editor

Published
2017
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29. Contributors

Author

Abolhassani, Hassan, primary, Aghamohammadi, Asghar, additional, Agulló, Pilar Llobet, additional, Ahanchian, Hamid, additional, Alyasin, Soheila, additional, Arshi, Saba, additional, Azizi, Gholamreza, additional, Barbouche, Mohamed-Ridha, additional, Bemanian, Mohammad Hassan, additional, Bousfiha, Aziz, additional, Chavoshzadeh, Zahra, additional, Cheraghi, Taher, additional, Crimi, Romina Dieli, additional, Cunningham-Rundles, Charlotte, additional, Dabbaghzadeh, Abbas, additional, Darougar, Sepideh, additional, Doffinger, Rainer, additional, Durandy, Anne, additional, Ehlayel, Mohammad, additional, Eibel, Hermann, additional, Eslamian, Mohammad Hossein, additional, Esmaeilzadeh, Hossein, additional, Espanol, Teresa, additional, Fallahpour, Morteza, additional, Fekrvand, Saba, additional, Gennery, Andrew R, additional, Ghaffari, Javad, additional, Ghaffari, Negar, additional, Gupta, Sudhir, additional, Hammarström, Lennart, additional, Heydrzadeh, Marzieh, additional, Kalantari, Arash, additional, Kalmarzi, Rasoul Nasiri, additional, Kanegane, Hirokazu, additional, Khalighi, Negar, additional, Khalili, Abbas, additional, Lavin, Martin, additional, Mahdaviani, Alireza, additional, Momen, Tooba, additional, Nabavi, Mohammad, additional, Niehues, Tim, additional, Ochs, Hans D., additional, Olbrich, Peter, additional, Plebani, Alessandro, additional, Rezaei, Nima, additional, Seif, Farhad, additional, Seppänen, Mikko, additional, Shabestari, Mahnaz Sadeghi, additional, Shafiei, Alireza, additional, Shariat, Mansoureh, additional, Suri, Deepti, additional, Tavakol, Marzieh, additional, van der Burg, Mirjam, additional, van Zelm, Menno, additional, Vosoughi Motlagh, Ahmad, additional, and Yazdani, Reza, additional

Published
2021
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30. Management of inborn errors of immunity

Author

Kalmarzi, Rasoul Nasiri, primary, Eslamian, Mohammad Hossein, additional, Abolhassani, Hassan, additional, Aghamohammadi, Asghar, additional, Hammarström, Lennart, additional, and Gennery, Andrew R., additional

Published
2021
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31. Preface

Author

Abolhassani, Hassan, primary, Yazdani, Reza, additional, Rezaei, Nima, additional, and Aghamohammadi, Asghar, additional

Published
2021
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32. Predominantly antibody deficiencies

Author

Cheraghi, Taher, primary, Kalantari, Arash, additional, Shabestari, Mahnaz Sadeghi, additional, Abolhassani, Hassan, additional, Eibel, Hermann, additional, Hammarström, Lennart, additional, Kanegane, Hirokazu, additional, Durandy, Anne, additional, Plebani, Alessandro, additional, Cunningham-Rundles, Charlotte, additional, and Aghamohammadi, Asghar, additional

Published
2021
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34. Comparison of Common Monogenic Defects in a Large Predominantly Antibody Deficiency Cohort

Author

Yazdani, Reza, Abolhassani, Hassan, Kiaee, Fatemeh, Habibi, Sima, Azizi, Gholamreza, Tavakol, Marzieh, Chavoshzadeh, Zahra, Mahdaviani, Seyed Alireza, Momen, Tooba, Gharagozlou, Mohammad, Movahedi, Masoud, Hamidieh, Amir Ali, Behniafard, Nasrin, Nabavi, Mohammamd, Bemanian, Mohammad Hassan, Arshi, Saba, Molatefi, Rasol, Sherkat, Roya, Shirkani, Afshin, Amin, Reza, Aleyasin, Soheila, Faridhosseini, Reza, Jabbari-Azad, Farahzad, Mohammadzadeh, Iraj, Ghaffari, Javad, Shafiei, Alireza, Kalantari, Arash, Mansouri, Mahboubeh, Mesdaghi, Mehrnaz, Babaie, Delara, Ahanchian, Hamid, Khoshkhui, Maryam, Soheili, Habib, Eslamian, Mohammad Hossein, Cheraghi, Taher, Dabbaghzadeh, Abbas, Tavassoli, Mahmoud, Kalmarzi, Rasoul Nasiri, Mortazavi, Seyed Hamidreza, Kashef, Sara, Esmaeilzadeh, Hossein, Tafaroji, Javad, Khalili, Abbas, Zandieh, Fariborz, Sadeghi-Shabestari, Mahnaz, Darougar, Sepideh, Behmanesh, Fatemeh, Akbari, Hedayat, Zandkarimi, Mohammadreza, Abolnezhadian, Farhad, Fayezi, Abbas, Moghtaderi, Mojgan, Ahmadiafshar, Akefeh, Shakerian, Behzad, Sajedi, Vahid, Taghvaei, Behrang, Safari, Mojgan, Heidarzadeh, Marzieh, Ghalebaghi, Babak, Fathi, Seyed Mohammad, Darabi, Behzad, Bazregari, Saeed, Bazargan, Nasrin, Fallahpour, Morteza, Khayatzadeh, Alireza, Javahertrash, Naser, Bashardoust, Bahram, Zamani, Mohammadali, Mohsenzadeh, Azam, Ebrahimi, Sarehsadat, Sharafian, Samin, Vosughimotlagh, Ahmad, Tafakoridelbari, Mitra, Rahim, Maziar, Ashournia, Parisa, Razaghian, Anahita, Rezaei, Arezou, Samavat, Ashraf, Mamishi, Setareh, Khazaei, Hossein Ali, Mohammadi, Javad, Negahdari, Babak, Parvaneh, Nima, Rezaei, Nima, Lougaris, Vassilios, Giliani, Silvia, Plebani, Alessandro, Ochs, Hans D., Hammarström, Lennart, and Aghamohammadi, Asghar

Published
2019
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37. Vaccine-Derived Poliovirus Infection among Patients with Primary Immunodeficiency and Effect of Patient Screening on Disease Outcomes, Iran

Author

Shaghaghi, Mohammadreza, Shahmahmoodi, Shohreh, Nili, Ali, Abolhassani, Hassan, Madani, Seyedeh Panid, Nejati, Ahmad, Yousefi, Maryam, Kandelousi, Yaghoob M., Irannejad, Mona, Shaghaghi, Shiva, Zahraei, Seyed Mohsen, Mahmoudi, Sussan, Gouya, Mohammad Mehdi, Yazdani, Reza, Azizi, Gholamreza, Parvaneh, Nima, and Aghamohammadi, Asghar

Subjects
United States. Centers for Disease Control and Prevention, Health screening, Vaccines, Disease eradication, Paralysis -- Patient outcomes, Immunodeficiency -- Patient outcomes, Medical research, Severe combined immunodeficiency, Intelligence gathering, Poliomyelitis, Health, World Health Organization
Abstract

During the 3 decades since the establishment of the Global Polio Eradication Initiative (GPEI), the use of oral poliovirus vaccine (OPV) and inactivated poliovirus vaccine (IPV) has led to a [...]

Published
2019
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46. Fourth Update on the Iranian National Registry of Primary Immunodeficiencies: Integration of Molecular Diagnosis

Author

Abolhassani, Hassan, Kiaee, Fatemeh, Tavakol, Marzieh, Chavoshzadeh, Zahra, Mahdaviani, Seyed Alireza, Momen, Tooba, Yazdani, Reza, Azizi, Gholamreza, Habibi, Sima, Gharagozlou, Mohammad, Movahedi, Masoud, Hamidieh, Amir Ali, Behniafard, Nasrin, Nabavi, Mohammamd, Bemanian, Mohammad Hassan, Arshi, Saba, Molatefi, Rasol, Sherkat, Roya, Shirkani, Afshin, Amin, Reza, Aleyasin, Soheila, Faridhosseini, Reza, Jabbari-Azad, Farahzad, Mohammadzadeh, Iraj, Ghaffari, Javad, Shafiei, Alireza, Kalantari, Arash, Mansouri, Mahboubeh, Mesdaghi, Mehrnaz, Babaie, Delara, Ahanchian, Hamid, Khoshkhui, Maryam, Soheili, Habib, Eslamian, Mohammad Hossein, Cheraghi, Taher, Dabbaghzadeh, Abbas, Tavassoli, Mahmoud, Kalmarzi, Rasoul Nasiri, Mortazavi, Seyed Hamidreza, Kashef, Sara, Esmaeilzadeh, Hossein, Tafaroji, Javad, Khalili, Abbas, Zandieh, Fariborz, Sadeghi-Shabestari, Mahnaz, Darougar, Sepideh, Behmanesh, Fatemeh, Akbari, Hedayat, Zandkarimi, Mohammadreza, Abolnezhadian, Farhad, Fayezi, Abbas, Moghtaderi, Mojgan, Ahmadiafshar, Akefeh, Shakerian, Behzad, Sajedi, Vahid, Taghvaei, Behrang, Safari, Mojgan, Heidarzadeh, Marzieh, Ghalebaghi, Babak, Fathi, Seyed Mohammad, Darabi, Behzad, Bazregari, Saeed, Bazargan, Nasrin, Fallahpour, Morteza, Khayatzadeh, Alireza, Javahertrash, Naser, Bashardoust, Bahram, Zamani, Mohammadali, Mohsenzadeh, Azam, Ebrahimi, Sarehsadat, Sharafian, Samin, Vosughimotlagh, Ahmad, Tafakoridelbari, Mitra, Rahimi, Maziar, Ashournia, Parisa, Razaghian, Anahita, Rezaei, Arezou, Mamishi, Setareh, Parvaneh, Nima, Rezaei, Nima, Hammarström, Lennart, and Aghamohammadi, Asghar

Published
2018
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49. Demographic, Clinical, and Immunological features in Combined Immunodeficiency Patients with Pulmonary Complications: A Retrospective Multicenter Study from Iran

Author

Khanbabaee, Ghamartaj, primary, Pourghasem, Matin, additional, Jamee, Mahnaz, additional, Tabatabaii, Seyed Ahmad, additional, Khalili, Mitra, additional, Mesdaghi, Mehrnaz, additional, Sadeghi-Shabestari, Mahnaz, additional, Shirvani, Armin, additional, Sadr, Saeid, additional, Zahmatkesh, Arefeh, additional, Delavari, Samaneh, additional, Eslami, Narges, additional, Farahbakhsh, Nazanin, additional, Mansouri, Mahboubeh, additional, Tabiei, Ebrahim, additional, Modarresi, Seyedeh Zalfa, additional, Behbahani, Abdolhamid Taghizadeh, additional, Eslamian, Golnaz, additional, Fallahi, Mazdak, additional, Enayat, Javad, additional, Fallah, Shahrzad, additional, Pourghasem, Mahsa, additional, Aghamohammadi, Asghar, additional, and Chavoshzadeh, Zahra, additional

Published
2023
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50. Immune Dysregulation Diseases

Author

Imashuku, Shinsaku, Erdős, Melinda, Al-Herz, Waleed, Bemanian, Mohammad Hassan, Kanegane, Hirokazu, Maródi, László, Mohammadinejad, Payam, Rosenzweig, Sergio D., Aghamohammadi, Asghar, Aghamohammadi, Asghar, editor, and Rezaei, Nima, editor

Published
2012
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