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Infantile myofibromatosis (IM) is the most common fibrous disorder of infancy and early childhood. Solitary intracranial involvement is rare and often unrecognized. This makes its early diagnosis and adequate management difficult. The majority of lesions are localized to the skull or dura with variable intracranial extension. Herein, we report a misdiagnosed and aggressive presentation of a solitary IM of the petrous bone. Our aim is to discuss histopathological differential diagnoses and management difficulties.

Renal cell carcinomas are tumors known for their metastatic potential. The lungs, the lymph nodes, the lungs, the spleen, the adrenal gland and the cervix remain the metastatic sites of predisposition. The symptoms of metastatic lesion may be due to the initial manifestation of renal malignancy. We report in this work a buccal localization of metastases from renal cell carcinoma to clear cells in a patient aged 65 years or less in our department of otolaryngology and cervical-facial surgery.

Frontal sinuses that present with abnormally large size are often clinically described as a deformity of the forehead, caused by Pneumosinus dilatans (PD). We report a rare case of Pneumosinus dilatans frontalis which was accidentally discovered by a paranasal sinus CT scan requested following frontal headaches, and thus revealing diffuse osteoporosis. Pneumosinus dilatans is often an unexpected radiological finding; however, in most cases, it is diagnosed by recognition of a frontal deformity.

Paraganglioma is a rare neuroendocrine tumor. Nasal localization is very rare. Head and neck paragangliomas represent only 0.6% of head and neck tumors and 3% of all paragangliomas. The treatment is based on surgery. Radiotherapy is indicated if the surgery does not provide complete resection. We report the case of a 36-year-old patient who has had left nasal obstruction with epistaxis for 2 years. The CT scan shows a solid mass centered on the left nasal cavity, puffy, without signs of aggression, benign-looking. The patient underwent a complete endoscopic endonasal tumor removal after preoperative external carotid embolization. Pathological analysis with immunohistochemistry confirmed the diagnosis of paraganglioma. The follow-up to the treatment was favorable.

La myiase est une maladie causee par les larves de mouches. La localisation auriculaire (otomyiase) est une affection rare, causee frequemment par les especes de la famille des sarcophages. Elle survient souvent sur des lesions chroniques negligees chez des personnes dont l´hygiene est precaire. Depuis longtemps au Maroc la myiase a ete decrite. Cependant, peu d´etudes epidemiologiques ont ete consacrees a cette affection. Nous rapportons dans ce travail l´observation de deux patientes recues et prises en charge aux Urgences d´Oto-rhino-laryngologie et de Chirurgie Cervico-faciale a l´Hopital des Specialites (CHIS), Rabat, Maroc.

Le syndrome de Lemierre « SL » est une maladie rare qui prend son origine tres souvent d´une infection oropharyngee se compliquant d´une thrombose septique de la veine jugulaire interne et d´emboles septiques a predominance pulmonaire dans sa forme typique. Dans notre cas, le SL n´est qu´un tableau revelateur d´un carcinome epidermoide de la bouche œsophagienne surinfecte. Tout retard diagnostic ou de prise en charge peut etre responsable d´une morbi-mortalite elevee. Son diagnostic repose sur : un faisceau d´arguments cliniques, radiologiques dont la TDM cervico thoracique avec injection du produit de contraste trouve tout son interet ainsi que sur des examens bacteriologiques surtout dans les formes atypiques. Le traitement est principalement medical base sur une antibiotherapie ciblee urgente et prolongee, l´anticoagulation reste tres discutee cas par cas, et le traitement chirurgical est reserve a des cas bien particuliers.

Objective To describe a case of inferior vestibular neuritis manifesting with a severe dizziness attack. To review available literature on the clinical features and characteristic presentation of this disease. Methods Case report with literature review. Results We report the case of a 54 years old female patient presenting with a severe vertigo without any other particular oto-neurological signs. The initial presentation simulated central vertigo, but the VHIT showed a left posterior canal deficit and the cVEMP was in favor of saccular involvement. All these elements would suggest an inferior vestibular neuritis. Conclusion Inferior vestibular neuritis is a diagnosis to be evoked in front of an atypical vertigo and to be confirmed by the VHIT and the VEMPs.

Kikuchi-Fujimoto's disease KFD is a rare and benign cause of cervical lymphadenopathy. It is an anatomoclinical entity of unknown etiology. The confirmation of the diagnosis is always provided by histological lymph node study. The clinical picture sometimes evokes lymphoma or tuberculosis. The evolution is generally favorable with spontaneous healing after a few weeks. We report the case of a 26-year-old woman who had consulted for cervical lymphadenopathy associated with fever. The cervical lymph node biopsy concluded to Kikuch-Fujimoto's disease. The evolution was marked by rapid regression of lymphadenopathy under corticosteroid treatment.

Rhinolithiasis is a rare condition often neglected or unknown that tends to disappear in developed countries and corresponds to a solid calcification by gradual deposition of calcareous salts around a central resorbable or non-resorbable foundation of varying shape and size. The most common symptom is a long-term unilateral purulent rhinorrhea and unilateral nasal obstruction. Nasal endoscopy and imaging are interesting for the positive diagnosis but especially to highlight the anatomical anomalies or related pathologies. Therapeutic management requires endonasal extraction of the rhinolith under general anesthesia. We report an observation of rhinolithiasis treated in our department associating a significant deformation of the nasal pyramid to osteolysis.

Introduction: Cervical lymph node involvement has a major impact on prognosis and treatment decisions in patients with upper aerodigestive tract (UADT) cancer.Objective: The aim of this study was to assess the incidence and pattern of cervical lymph node (LN) metastases in cancers of the upper aerodigestive tractMethods: This prospective study was conducted by the Department of ENT and Maxillofacial Surgery at Specialities University Hospital of Rabat, collecting data between October 2009 and December 2011. Lymph nodes were counted, clinically and radiologically localized, excised, then studied histologically.Results: During this period, 106 patients have been treated surgically with a recent diagnosis of UADT cancer. The average age of our patients was 55±13.3 years, while male/female ratio was 3.5 to 1. More than half of our patients were operated with cancer of the larynx (58.5%, n=62); 27.4% (n=29) of patients suffered from oral cavity cancer and 14.2% (n=15) had cancer of the hypopharinx. Cervical lymph node invasion was estimated at 31.2% clinically, and 38.7% radiologically and histologically, distributed in different sites.Although the percentage of the invasion is almost similar clinically, radiologically and histologically, the high number of false positives and true negatives according to clinical and radiological exams confirms that specificity and sensitivity of these two exams is still poor compared to histology.Conclusion: Thus, cervical metastases have to be diagnosed histologically. Moreover, the low percentage of lymph node invasions in the case of a UADT cancer suggests that the use of sentinel lymph node technique could be important, as it has been validated for small T1T2N0 tumors in the oral cavity. Further studies are needed to confirm its validity in case of other UADT tumor types.

Kartagener syndrome is an autosomal recessive genetic ciliary disorder comprising of a classic triad of sinusitis, situs inversus and bronchiectasis. It's the one of primary ciliary dyskinesia disorders with manifestations present from childhood. Most patients of PCD have situs inversus. We present a case of 18 year-old women with recurrent lower and upper respiratory tracts infections, and rhinolalia clausa.Pan African Medical Journal 2016; 23

Le syndrome de Gorlin et Goltz est une affection hereditaire, a transmission autosomique dominante, due a une mutation du gene PTCH ayant pour localisation chromosomique 9q 22.3-q31. C’est un syndrome rare qui se caracterise par un spectre d’anomalies du developpement et par une predisposition a differents cancers. La complexite des signes cliniques a conduit a etablir des criteres specifiques pour faciliter le diagnostic. La prise en charge therapeutique est symptomatique, avec une surveillance carcinologique rigoureuse. Nous rapportons une nouvelle observation de syndrome de Gorlin et Goltz chez un adolescent de 17 ans et, a travers une revue de litterature, nous discutons les principales caracteristiques de cette rare affection. Med Buccale Chir Buccale 2007 ; 13 : 97-101.

Presenteration d’un cas documente d'un angiolipome de la region submandibulaire et des donnees recentes de la litterature sur ce sujet. Il s’agit d’un patient âge de 22 ans avec une tumefaction evoluant depuis 8 ans dans la region submandibulaire gauche qui s’est revelee, a l’examen anatomopathologique, apres exerese chirurgicale complete, etre un angiolipome. Apres trois ans de recul, il n’y a aucun signe de recidive tumorale. L'angiolipome de la region cervicale, en particulier de la region submandibulaire est extremement rare. Le tableau clinique peut faire evoquer une pathologie de la glande submandibulaire. L’origine extra-glandulaire de la lesion est en general facilement precisee par les donnees de l’imagerie. L’exerese chirurgicale est parfois difficile car il existe une forme infiltrante d’angiolipome. (Med Buccale Chir Buccale 2006 ; 12 : 171-174).

Le kyste epidermoide du plancher buccal est une tumeur benigne et rare. Histologiquement, la paroi kystique est constituee par un epithelium malpighien pluristratifie, keratinisant, et le contenu de la cavite est compose par des squames de keratine. L’aspect histologique est bien different de celui des autres kystes de type dermoide ou teratoide. C’est un patient âge de 23 ans qui presentait une tumefaction du plancher buccal et de la region sus-hyoidienne. D’evolution lente, cette tumefaction etait a l’origine de troubles de l’elocution et de la mastication. L’echographie, completee par l’examen tomodensitometrique, a mis en evidence une masse kystique, echogene et bien limitee. Le traitement a consiste en une exerese chirurgicale par voie endobuccale ; l’aspect macroscopique et l’examen histologique ont permis de preciser qu’il s’agissait d’un kyste epidermoide. Les differents caracteres de ce cas sont identiques a ceux retrouves dans la litterature. (Med Buccale Chir Buccale 2006 ; 12 : 175-8).

Plemorphic adenoma is a frequent benign tumor of the major salivary glands. It could also develop from accessory salivary glands. We are reporting an extremely rare case of pleomorphic adenoma developing from the infratemporal space. The final diagnosis was based on histological confirmation. The treatment was mainly a complete resection via an anterior transmaxillary approach. Diagnosis, clinical behaviour, and treatment of pleomorphic adenoma of the infra-temporal space are reviewed from the literature.

Primary hydatid cyst of thyroid gland is an exceptional localization even in Morocco where echinococcal disease is endemic. A 23-year-old woman presented with multiples cystic lesions of the thyroid revealed by neck mass and dyspnea. She underwent a subtotal thyroidectomy. The diagnosis of hydatid cyst was made preoperatively and was confirmed by histological studies. Further investigation failed to identify any other evidence of systemic hydatidosis. The patient has remained asymptomatic for 24 months after surgery. The possibility of hydatid disease, though rare, should be always kept in mind, for patients with cystic lesions of the thyroid, because a needle aspiration biopsy is a potentially harmful procedure.