1. Survival time in cystinosis. A collaborative study.
- Author
-
Gretz N, Manz F, Augustin R, Barrat TM, Bender-Götze C, Brandis M, Bremer HJ, Brodehl J, Broyer M, Bulla M, Callis L, Chantler C, Diekmann L, Dillon MJ, Egli F, Ehrich JH, Endres W, Fanconi A, Feldhoff C, Geisert J, Gekle D, Geschöll-Bauer B, Grote K, Grüttner R, Hagge W, Haycock CB, Hennemann H, Klare B, Leupold D, Löhr H, Michalk D, Oliveira A, Ott F, Pistor K, Rau J, Schärer K, Schindera F, Schmidt H, Schulte-Wissermann H, Verrier-Jones K, Weber HP, Willenbockel U, and Wolf H
- Subjects
- Adolescent, Adult, Child, Child, Preschool, Cystinosis therapy, England, Female, France, Germany, West, Humans, Male, Portugal, Retrospective Studies, Sex Factors, Spain, Switzerland, Time Factors, Cystinosis mortality
- Abstract
In a retrospective study the overall survival time of 205 cystinotic patients of six countries was determined. The median survival time was 8.5 years. The median time for 'renal death' (age at death due to uraemia or age at starting renal replacement therapy) was 9.2 years. The youngest patient dying of renal death was 5.2 years. No sex difference in survival time was noticed. Furthermore no difference in survival time was noted between the different countries. The analysis of the overall survival curve indicates no clear differences between the infantile and adolescent types of cystinosis.
- Published
- 1983