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This citation analysis examines the use of Spanish- and Portuguese-language books and articles in PhD dissertations on Latin America at the University of New Mexico between 2000 and 2009. Two sets of data are presented: The first identifies the use of Spanish- and Portuguese-language books and articles across 17 academic departments; and the second analyzes how well local holdings meet demands for a select geographical area--Mexico. These local data contradict conclusions in general citation studies of the humanities, social sciences and foreign languages. They prove that preconceived ideas about foreign language usage from general citation studies do not provide reliable templates for local acquisition decisions. Librarians need to look at their research communities and local usage habits instead of relying on general studies for answers.

Mucopolysaccharidosis (MPS) VII or Sly syndrome, caused by deficiency of the b-glucuronidase enzyme (GUSB), is a rare form of MPS. As is true for several other lysosomal storage disorders, patients with MPS VII show wide clinical variability, with severe, intermediate and attenuated presentations. Forty-one different disease-causing mutations have been identified in patients from Japan, Europe, the U.S., Northern Africa, Kuwait, India, Mexico and Chile. Although L176F is the most common mutation in the GUSB gene, accounting for approximately 20% of the mutant alleles, few L176F patients have been described in the literature. Though rare, MPS VII should be investigated in patients with clinical and radiological signs of a lysosomal storage disease.