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An encyclopedia entry for "Unverricht-Lundborg Disease" is presented. The disease also known as Baltic myoclonus was first described in 1891 and serves as the protoype of the progressive myoclonus epilepsies. It relates the high incidence of the disease among people in the Baltic Sea and Mediterranean regions, as well as Estonia, Finland and southeast Sweden. It outlines the features of this progressive myoclonic epilepsy (PME). It describes the impact of cystatin B on the disease.

An encyclopedia entry for "Jansky-Bielchowski disease" is presented. It refers to late infantile form of neuronal ceroid-lipofuscinoses (NCL), seen prominently in patients from Finland. The disease, which is associated with autosomal recessive transmission, occurs at age 2-4 years, and the seizures are usually composed of massive myoclonic jerks triggered by sensory stimuli.

An encyclopedia entry for "Santavuori-Haltia disease" is presented. It refers to a disease in an early infantile form of neuronal ceroid lipofuscinoses that is rarely seen outside Finland. The disease presents at one-and-a-half years of age and is characterized by myoclonus, ataxia, visual impairment with optic atrophy.

An encyclopedia entry for "Baltic myoclonus" is presented. It refers to a progressive form of myoclonic epilepsy discovered in Finland and affects 1 in 20,000. It notes that generalized tonic-clonic seizures are often observed in patients with Baltic myoclonus. Myoclonic movements may be triggered by stress and sensory stimuli.