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Mesenchymal hamartomas of the liver is considered a benign tumour, although it provides significant challenges in the diagnosis and operative management. Clinical features, laboratory results and radiographic imaging are often non-specific and inconclusive. Thus, it is still difficult to differentiate from malignant lesion without pathological examination. While this tumour is usually diagnosed in the first 2 years of life, few cases in older children have been reported and most of them are case reports. In this article, we want to report our clinical evaluation, results of image diagnosis, surgical procedure and the follow-up simultaneously we discuss the possible differential diagnosis of such a case at this age.

Total colonic aganglionosis is the most rare form of Hirschsprung's disease and is defined as the absence of ganglion cells in both myenteric and submucosal plexus extending from the anus to at least the ileocecal valve. Intrauterine intussusceptions, on the second hand, is also extremely rare. It may occur in late stage of pregnancy and cause impairment of blood supply to a segment of intestine leading to its resorption and atresia. The coexistence of total colonic Hirschsprung's disease, intrauterine intussusception and ileal atresia has yet to be described in the literature.We present this rare case of intrauterine intussusception causing an association of ileal atresia and total colonic Hirschsprung's disease. The diagnosis was performed per-operatively.

Hydatid disease is a cosmopolitan anthropozoonosiss, common to both humans and mammals, is caused by infection with the larval stage of Echinococcus granulosus. It occurs worldwide and is especially common in endemic countries. Hydatid cysts are most commonly found in the liver and lungs.Primary hydatid cysts are rarely detected in muscle tissue, even in endemic countries, it represents less than 1% of all locations of cystic echinococcosis. Clinical signs are often non-specific early on and there are no pathognomonic radiologic features, thus making it difficult to diagnose.Hydatid disease is still considered a major public health issue and must be suspected in front of any cystic musclar mass.We report an unusual case of isolated hydatid cyst in pectoralis muscle without pulmonary or pleural involvement, in a 14-year-old patient, whose pre-operative imagery suggested a cystic lymphangioma and the diagnosis of musclar hydatid cyst was made intra-operatively and confirmed by an anatomopathological examination.

Congenital bronchopulmonary foregut malformation (CBPFM) is a rare congenital malformation involving both the digestive and the respiratory system. Esophageal lung is an entity belonging to this group. Few cases have been reported. Diagnostic can be a challenge in some case. Much closer cooperation between pediatric surgeons and radiologists is essential to all investigations of these congenital malformations in particular to those associated to other congeniatl abnormality.Herein we describe the diagnostic and therapeutic approach in a six months old girl with esophageal lung.associated to dextrocardia.

Transverse testicular ectopia(TTE) is a rare anomaly defined by the presence of both testis in the same hemiscrotum or in the same inguinal canal.The main treatment of TTE is surgical intervention.Here we report a case of type 2 transverse testicular ectopia in an eight months old child.The boy had a right side inguinal hernia and a non-palpable testis on the left side. Ultrasonography confirmed the presence of both testis at the right inguinal region.Our case was associated with the persistence of Mullerian duct.After the excision of the Mullerian duct remnant, bilateral orchiopexy was performed.

We report a case of an unusual trichobezoar called Rapunzel syndrome in a 12 year-old-girl diagnosed presurgically with the use of ultrasonography, CT scan and endoscopy. The removal of the mass was performed by a gastrotomy through a mini-laparotomy incision. We want to describe the case of a preadolescent female patient with Rapunzel syndrome and its management, given that it is a rare condition and few cases have been reported in our country.

Hydatid disease or hydatidosis is a worldwide zoonosis disease caused by the tapeworm of Echinococcus granulosus and still widely endemic in Tunisia especially in rural areas where the sheep-dog cycle is dominant. It is an important public health problem in the pediatric age group causing significant morbidity and mortality. We report a case of primary hydatid cyst of the small intestine in a child and we want to highlight the difficulty that we meet in diagnostic despite the contribution of imaging.

Hydatid disease or hydatidosis is a worldwide zoonosis disease caused by the tapeworm of Echinococcus granulosus and still widely endemic in Tunisia especially in rural areas where the sheep-dog cycle is dominant. It is an important public health problem in the pediatric age group causing significant morbidity and mortality. We report a case of primary hydatid cyst of the small intestine in a child and we want to highlight the difficulty that we meet in the diagnosis despite the contribution of imaging. [ABSTRACT FROM AUTHOR]