1. Agenesis of the dorsal pancreas presenting with diabetic ketoacidosis – a case report and literature review
- Author
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Xudan Yang, Jun Mo, Tian Yang, and Luping Wang
- Subjects
Adult ,Male ,medicine.medical_specialty ,Abdominal pain ,Diabetic ketoacidosis ,Endocrinology, Diabetes and Metabolism ,Case Report ,lcsh:Diseases of the endocrine glands. Clinical endocrinology ,Gastroenterology ,Agenesis of the dorsal pancreas ,Congenital Abnormalities ,03 medical and health sciences ,0302 clinical medicine ,Diabetes mellitus ,Glucose Metabolism Disorder ,Internal medicine ,C-peptide release test ,medicine ,Humans ,Pancreas ,lcsh:RC648-665 ,business.industry ,Metabolic acidosis ,General Medicine ,medicine.disease ,Prognosis ,medicine.anatomical_structure ,030220 oncology & carcinogenesis ,Ketonuria ,Pancreatitis ,medicine.symptom ,business ,030217 neurology & neurosurgery - Abstract
Background Agenesis of the dorsal pancreas (ADP) is clinically rare, and it is usually accompanied by abdominal pain. Various disorders of glucose metabolism associating with ADP have been reported, but there are only two studies reporting a correlation between ADP and DKA in English literature. Case presentation We present a case of a patient with ADP accompanied by abdominal pain and diabetic ketoacidosis as the initial clinical presentation. A 30-year-old man presented with a 3-month history of recurrent onset of persistent mild epigastric pain, which worsen when eating. Laboratory tests revealed metabolic acidosis, hyperglycemia, and ketonuria. Phase contrast CT and MRCP showed the absence of the body and tail of the pancreas, as well as the dorsal pancreatic duct. The C-peptide release test indicated β-cell dysfunction. A combination therapy of insulin, pancreatic enzyme supplements, and mosapride citrate were administrated and the pain gradually resolved. Conclusions As glucose metabolism disorders can vary across different individuals, we advise clinicians to consider the diagnosis of ADP for a patient who presents with a glucose metabolism disorder accompanied by abdominal pain, pancreatitis or steatorrhea.
- Published
- 2019