1. Moyamoya disease presenting as thalamic hemorrhage in a patient with neuromyelitis optica and Sjögren's syndrome.
- Author
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Asai Y, Nakayasu H, Fusayasu E, and Nakashima K
- Subjects
- Autoantibodies blood, Biomarkers blood, Cerebral Angiography, Cerebral Hemorrhage diagnosis, Cerebral Hemorrhage immunology, Cerebral Hemorrhage therapy, Female, Humans, Magnetic Resonance Imaging, Middle Aged, Moyamoya Disease diagnosis, Moyamoya Disease immunology, Moyamoya Disease therapy, Neurologic Examination, Neuromyelitis Optica diagnosis, Neuromyelitis Optica immunology, Neuromyelitis Optica therapy, Paraplegia etiology, Predictive Value of Tests, Sjogren's Syndrome diagnosis, Sjogren's Syndrome immunology, Sjogren's Syndrome therapy, Thalamic Diseases diagnosis, Thalamic Diseases immunology, Thalamic Diseases therapy, Time Factors, Tomography, X-Ray Computed, Cerebral Hemorrhage etiology, Moyamoya Disease complications, Neuromyelitis Optica complications, Sjogren's Syndrome complications, Thalamic Diseases etiology
- Abstract
A 52-year-old woman was admitted to the hospital with right thalamic hemorrhage. A carotid angiogram revealed occlusion of the terminal portions of the bilateral internal carotid arteries with basal moyamoya vessels, which was diagnosed as moyamoya disease (MMD). At 31 years of age, she was diagnosed with multiple sclerosis because of optic neuritis and myelitis. Paraplegia appeared 14 days after admission. T2-weighted thoracic magnetic resonance imaging revealed a high intensity lesion extending from T4 to T6. Her left upper limb was partially paralytic and her lower limbs exhibited paraplegia and dysesthesia. Anti-aquaporin 4 and anti-Sjögren's syndrome-A and -B antibodies were positive. The pathogenesis of neuromyelitis optica may be associated with such immunologic factors, but there are no reports of simultaneous presentations of neuromyelitis optica and MMD. Autoimmunity may be associated with the etiology of MMD., (Copyright © 2012 National Stroke Association. Published by Elsevier Inc. All rights reserved.)
- Published
- 2012
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