1. A lymphoproliferative pericardial mass
- Author
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Ximena Solis, Kenneth Nugent, Haneen Mallah, Andres Yepes-Hurtado, John Makram, Myrian Vinan-Vega, Barbara Mantilla, Pablo Paz, and Safaa Labib
- Subjects
Pathology ,medicine.medical_specialty ,Case Studies ,business.industry ,hemic and lymphatic diseases ,Castleman disease ,Medicine ,Mediastinal mass ,General Medicine ,Variable presentation ,business ,medicine.disease - Abstract
Castleman disease (CD) is a rare lymphoproliferative disorder with variable presentation and prognosis. Most CD cases are unicentric and correspond to the hyaline-vascular variant, a histopathological classification associated with better outcomes, which commonly presents as an enhancing hypervascular mediastinal mass. CD is often asymptomatic and surgically resectable. Nonetheless, surgical resection can be difficult when the lymphoid mass is causing compression of vital structures. We discuss a rare case of hyaline-vascular unicentric CD presenting as an incidental pericardial mass.
- Published
- 2020