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Originally recognized by Cushing and Bailey, hemangioblastoma is a developmental vascular neoplasm that is predominantly found in the posterior fossa. It is a highly vascularized tumor, with well-differentiated histologic features. Although rare, it remains the most common primary tumor of cerebellum in adults, along with metastases. MRI is the gold standard, allowing a precise characterization of the lesion's features, and its relationship with the surrounding structures. We report the case of a patient with a cerebellar symptomatology, in whom brain MRI raises the diagnosis of hemangioblastoma, which was then confirmed by histopathologic examination.

Muscle metastases of bronchopulmonary cancer are rare, notably when they are revealing. They can affect all muscles of the body with a predominance of psoas, diaphragmatic and para-vertebral muscles. We report a case of psoas muscle metastasis revealing bronchopulmonary cancer in a 40-year-old patient with a long history of smoking (30 packs of cigarettes/year) presenting a chronic left low back pain with asthenia and weight loss (15 kg/year). The clinical examination was unremarkable. An abdominal computed tomography scan showing a retroperitoneal mass at the expense of the left psoas muscle, lysing the L2 vertebral and left pedicle with intraspinal extension. A complement by cervico-thoracic computed tomography scan showed a lung mass with hilar and mediastinal lymphadenopathy. A scan-guided biopsy puncture of the psoas muscle mass identified its metastatic origin. The clinical picture is often deceptive leading to diagnostic and therapeutic delay, hence the interest of the imagery as well as histological confirmation is recommended.

Intraspinal synovial cysts are rare, we report a case of intraspinal lumbar synovial cyst discovered by sciatica, explored by CT and MRI we describe the radiological features to retain the diagnosis and choose the appropriate therapeutic modality.

Renal angiomyolipomas are rare type of benign renal neoplasm. They are composed of vascular, smooth and fat elements and can be associated to phacomatosis as Tuberous Sclerosis disease. Symptomatic presentation is most frequently spontaneous retroperitoneal hemorrhage, which can be fatal. The risk of bleeding is proportional to the size of the lesion (>4 cm of diameter). Typical angiomyolipomas are benign but may have alarming properties: nuclear pleomorphism and mitotic activity, extension into the vena cava, and spread to regional lymph nodes without malignant progression. We report a Computed Tomography finding of a rare giant bilateral angiomyolipomas with spontaneous hemorrhage and inferior vena cava thrombus in a patient with tuberous sclerosis, emphasizing the importance of imagery in the positive and etiologic diagnosis.

Gallstone ileus is a rare cause of acute abdomen, representing less than 1% of intestinal obstruction. It is due to mechanical small bowel obstruction (SBO) by a migrated gallstone. we report this observation to illustrate the imaging findings especially in CT scan. A 62-year-old woman was admitted to emergency for acute bowel obstruction. The CT scan has confirmed jejunal bowel distension with fluid levels upstream endoluminal formation which was rounded and well limited, measuring 5 cm of long axis. This training was slightly hyperdense with hypodense areas of fat density. Moreover, there was aerobilia with multiple fistulas between the duodenum (D1) and gallbladder, which was empty. The triad of aerobilia, small bowel obstruction and migrant gallstone was suggestive of gallstone ileus diagnosis. The patient was operated with good evolution. Gallstone ileus is an uncommon presentation of gallstone disease. It is frequently observed in elderly patients with a history of cholelithiasis or cholecystitis. Early diagnosis is crucial and would avoid morbidity and mortality related to this disease. CT scan shows the classical triad of Rigler with pneumobilia, an ectopic stone and mechanical ileus. CT may improve the diagnosis providing important information regarding the exact number, size, and location of ectopic stones and the site of intestinal obstruction or direct visualization of a biliary–enteric fistula, to help clinicians in the therapeutic management of patients.

La myosite ossifiante circonscrite (MOC) est une pathologie rare caractérisée par une ossification hétérotopique non tumorale des tissus mous. C’est une pathologie du sujet jeune, survenant le plus souvent après un traumatisme. Sa localisation est ubiquitaire, prédominante au niveau des ceintures et des membres. Nous rapportons l’observation d’une jeune patiente présentant une MOC paravertébrale sans contexte traumatique, dans le but de rappeler les critères diagnostics et les aspects en imagerie.The Pan African Medical Journal 2016;24

Malignant transformation of perineal fistula in Crohn's disease has rarely been reported. We report a case of Crohn's disease with recurrent perineal fistulas. A 36-year-old male, diagnosed with Crohn's disease at the age of 24, developed adenocarcinoma in an anorectal fistula that had existed for years. He was treated with adjuvant chemoradiotherapy but died. A high index of suspicion and regular surveillance is recommended in chronic anorectal fistulas in Crohn's disease. The shorter duration of Crohn's fistulas prior to malignant degeneration necessitates an aggressive approach to rule out cancer.Key words: Crohn´s disease, perianal disease, perineal adenocarcinoma

Sandhoff disease is a rare and severe lysosomal storage disorder representing 7% of GM2 gangliosidoses. Bilateral thalamic involvement has been suggested as a diagnostic marker of Sandhoff disease. A case of an 18-month-old infant admitted for psychomotor regression and drug resistant myoclonic epilepsy is presented. Cerebral CT scan showed bilateral and symmetrical thalamic hyperdensity. MRI revealed that the thalamus was hyperintense on T1-weighted images and hypointense on T2-weighted images with a hypersignal T2 of the white matter. Enzymatic assays objectified a deficiency of both hexosaminidases A and B confirming the diagnosis of Sandhoff disease.

A 9-year-old female presented to the emergency department complaining of intense peri-umbilical pain with nausea and vomiting after a road accident. Physical examination revealed abdominal tenderness with a painful well-circumscribed mass in the lower abdomen. The haemodynamic state was stable. Ultrasonography showed a mobile hypoechoic mass with a moderate amount of free intraperitoneal fluid. An abdominal CT scan was performed. Axial images before and after intravenously administered contrast material are shown. What are the abnormalities seen in Figure 1? Figure 1 Abdominal CT scans obtained before and after intravenously administered contrast material. What do you notice in Figure 2? Figure 2 Abdominal CT scan with intravenously administered contrast material at a higher level. What is your diagnosis?

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Resume La maladie de Carrington ou pneumopathie chronique idiopathique a eosinophile est une pathologie rare ne presentant que 0 a 2,5 % des pneumopathies infiltrantes diffuses. Elle est caracterisee par des infiltrats pulmonaires associes a une eosinophilie circulante et/ou alveolaire. Nous rapportons deux observations chez des femmes d’âge moyen dans le but de rappeler les elements du diagnostic positif en particulier les aspects radiologiques.