1. Right Ventricle Exclusion in Severe Neonatal Ebstein's Anomaly
- Author
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Woong-Han Kim, Jin-Ho Choi, Yong-Won Seong, Youngok Lee, Sun Kyung Min, and Sung Joon Park
- Subjects
Pulmonary and Respiratory Medicine ,congenital, hereditary, and neonatal diseases and abnormalities ,medicine.medical_specialty ,business.industry ,medicine.disease ,Surgery ,Shunt (medical) ,medicine.anatomical_structure ,Ventricle ,Internal medicine ,Ductus arteriosus ,Ebstein's anomaly ,cardiovascular system ,Heart murmur ,Cardiology ,Medicine ,Right atrium ,cardiovascular diseases ,medicine.symptom ,Cardiology and Cardiovascular Medicine ,business ,Pulmonary atresia ,Cavopulmonary shunt - Abstract
A one-day-old baby was transferred for cyanosis and heart murmur. Echocardiographic evaluation revealed that he had severe neonatal Ebstein’s anomaly (Carpentier type C), pulmonary atresia, and pulmonary circulation via patent ductus arteriosus. Because the wall of the atrialized right ventricle was very thin, showed decreased contractility, and the small right ventricle showed pulmonary atresia, we decided that a two-ventricular repair was impossible. When the patient was one-month-old, he underwent right atrium reduction-plasty, a right ventricular exclusion procedure (including atrialized right ventricle resection and functional right ventricle plication), and right modified Blalock-Taussig shunt. He was discharged without specific problems. He received a bidirectional cavopulmonary shunt successfully at 4 months later.
- Published
- 2010