1. Congenital intrahepatic arterioportal fistula presenting as severe undernutrition and chronic watery diarrhea in a 2-year-old girl.
- Author
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Tannuri AC, Tannuri U, Lima FR, Ricardi LR, Leal AJ, and da Silva MM
- Subjects
- Arteriovenous Fistula diagnosis, Arteriovenous Malformations diagnosis, Arteriovenous Malformations surgery, Child, Child Nutrition Disorders diagnosis, Child Nutrition Disorders therapy, Embolization, Therapeutic methods, Esophageal and Gastric Varices surgery, Female, Gastrointestinal Hemorrhage surgery, Humans, Hypertension, Portal surgery, Ligation methods, Treatment Outcome, Vipoma diagnosis, Vipoma therapy, Arteriovenous Fistula surgery, Hepatectomy methods, Hepatic Artery abnormalities, Hepatic Artery surgery, Portal Vein abnormalities, Portal Vein surgery
- Abstract
Intrahepatic arterioportal fistula (IAPF) is a rare cause of portal hypertension in young children. We report the case of a 2-year-old girl with severe undernutrition, chronic watery diarrhea, and gastrointestinal bleeding because of a congenital intrahepatic arterioportal fistula. Radiographic embolization and surgical ligation of the left hepatic artery were attempted, with no resolution of the symptoms. So, a left lobectomy was performed, with excellent results and prompt disappearance of the diarrhea. Hepatectomy should be considered as a definitive and reliable therapy for congenital IAPF.
- Published
- 2009
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