1. [Hyperplasia of adrenal rests in the testicle: a rare cause of male infertility].
- Author
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san Miguel Fraile P, Fernández Fernández G, Meijide Rico F, Antón Badiola I, Ortiz-Rey JA, Alvarez Alvarez C, and de la Fuente Buceta A
- Subjects
- 17-alpha-Hydroxyprogesterone blood, Adrenal Hyperplasia, Congenital blood, Adrenocorticotropic Hormone blood, Adult, Biopsy, Choristoma diagnosis, Choristoma diagnostic imaging, Choristoma pathology, Diagnosis, Differential, Diagnostic Errors, Humans, Hydrocortisone blood, Leydig Cell Tumor diagnosis, Magnetic Resonance Imaging, Male, Steroid 21-Hydroxylase genetics, Steroid 21-Hydroxylase metabolism, Testicular Diseases diagnosis, Testicular Diseases diagnostic imaging, Testicular Diseases pathology, Testicular Neoplasms diagnosis, Ultrasonography, Adrenal Glands, Adrenal Hyperplasia, Congenital complications, Choristoma complications, Infertility, Male etiology, Testicular Diseases complications
- Abstract
We report the case of a 37-year-old man with infertility caused by bilateral testicular masses secondary to congenital adrenal hyperplasia (21-hydroxylase deficiency). Testicular biopsy was done and its was initially interpreted as Leydig cell tumor but after clinical information was histologically reclassified as tumor of the adrenogenital syndrome. The differential diagnosis with Leydig cell tumor is discussed and it must be established through the clinical, biochemical, radiological and pathological features.
- Published
- 2003
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