1. [Intra-abdominal desmoplastic small round-cell tumors. An entity among peritoneal carcinomatoses in young adults].
- Author
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Roques B, Pichon A, De Laroche G, Garnier JF, and Jacquin JP
- Subjects
- Abdominal Neoplasms complications, Abdominal Pain etiology, Adolescent, Adult, Antineoplastic Combined Chemotherapy Protocols therapeutic use, Carcinoma complications, Carcinoma, Small Cell complications, Chemotherapy, Adjuvant, Cisplatin administration & dosage, Doxorubicin administration & dosage, Etoposide administration & dosage, Fatal Outcome, Humans, Ifosfamide administration & dosage, Male, Middle Aged, Treatment Outcome, Abdominal Neoplasms diagnosis, Abdominal Neoplasms surgery, Carcinoma diagnosis, Carcinoma surgery, Carcinoma, Small Cell diagnosis, Carcinoma, Small Cell surgery
- Abstract
Desmoplastic small round-cell tumors in young adults were first described in 1989. They may be revealed by an abdominal mass or a peritoneal carcinomatosis. The diagnosis and the initial treatment are based on debulking surgery. Chemotherapy using doxorubicin, ifosfamide, etoposide and cisplatin can then be proposed. Despite some initial chemosensitivity, prognosis remains poor.
- Published
- 2000