1. Systemic lupus erythematosus associated with moyamoya syndrome
- Author
-
K M El Ramahi and H M Al Rayes
- Subjects
Male ,medicine.medical_specialty ,Adolescent ,030204 cardiovascular system & hematology ,Brain Ischemia ,03 medical and health sciences ,0302 clinical medicine ,Rheumatology ,immune system diseases ,medicine.artery ,Internal medicine ,Occlusion ,Medicine ,Humans ,Lupus Erythematosus, Systemic ,Carotid Stenosis ,Moyamoya disease ,skin and connective tissue diseases ,Cyclophosphamide ,030203 arthritis & rheumatology ,medicine.diagnostic_test ,Aspirin ,business.industry ,Anticoagulants ,Brain ,medicine.disease ,Collateral circulation ,Magnetic Resonance Imaging ,Cerebral Angiography ,Paresis ,Treatment Outcome ,Angiography ,Ischemic stroke ,Cardiology ,Prednisone ,Internal carotid artery ,Moyamoya Disease ,business ,Carotid Artery, Internal ,Papular mucinosis ,Cerebral angiography - Abstract
Moyamoya disease is an uncommon clinical entity, characterized by bilateral occlusion of the internal carotid artery and the development of collateral arteries. An 18-year-old Saudi male with systemic lupus erythematosus (SLE) presented with mild right hemiparesis, followed by recurrent ischemic stroke. Cerebral angiography showed bilateral internal carotid artery stenosis associated with the development of collateral circulation (moyamoya vessels). There was no evidence of active SLE or other risk factors for cerebral occlusion, such as antiphospholipid antibody syndrome. Medical and surgical interventions did not influence the poor outcome of the recurrent ischemic insults.
- Published
- 2000