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Abstract: To report on the outcomes of sequential bilateral cochlear implantation (CI) in children with inner ear malformation. The study design is a retrospective case study. The setting is a tertiary reference center. Two children presenting a profound bilateral congenital hearing loss with bilateral hypoplasia of the cochleovestibular nerves and hypoplasic external semicircular canal had a cochlear implant at respectively 16 months and 33 months. A second implant was proposed at respectively 17 and 20 months after the first implant. The main outcome measures are audiometry, perceptive results in closed and open set words (CSW and OSW) and oral production at follow-up. The first cochlear implant gave respectively mean thresholds at 60dB and 70dB. Bilateral CI showed mean threshold at respectively 40dB and 55dB. In case 1, perceptive assessment was 83% and 70% in respectively CSW and OSW with oral production and comprehension of sentences after 1 year follow-up. In case 2, the perceptive assessment showed no perceptive or linguistic evolution at 6 months follow-up. In cochleovestibular nerve hypoplasia, bilateral implantation could be discussed in cases of limited result after unilateral implant. [Copyright &y& Elsevier]

Summary: Introduction: Congenital epulis is a rare benign tumor that originates from the mucosa of the dental alveolar ridge. Management of congenital epulis is unclear; most authors recommend surgical excision during infancy. Case report: We report a case of congenital epulis arising from the anterior mandibular region that was managed conservatively. This epulis did not interfere with breast-feeding or respiration. Subsequently, there was spontaneous involution of the lesion during the 1st year of life. Conclusion: Small and medium congenital epulis (<20mm) exceptionally compromises feeding and might regress spontaneously. Subsequently, conservative treatment should be adopted. Surgical treatment should be indicated only when major feeding or respiratory problems are present or when the clinical diagnosis is uncertain. [Copyright &y& Elsevier]