1. Ampullary somatostatinoma in a patient with von Recklinghausen's disease.
- Author
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Kainuma, Osamu, Ito, Yasushi, Taniguchi, Tetsushi, Shimizu, Takanori, Nakada, Hisashi, Date, Yoko, Hara, Tsuyoshi, Kainuma, O, Ito, Y, Taniguchi, T, Shimizu, T, Nakada, H, Date, Y, and Hara, T
- Abstract
We report a case of somatostatinoma of the ampulla of Vater associated with von Recklinghausen's disease in a 44-year-old woman. On admission the patient was jaundiced, and percutaneous Cholangio-drainage was performed. Cholangiography revealed stenosis of the common bile duct at the lower end Duodenoscopy showed a yellowish tumor of the ampulla of Vater, and the biopsy specimens showed no malignant cells. Pylorus-preserving pancreaticoduo-denectomy was performed. Histologically, the tumor was composed of small round cells with a solid or trabecular pattern and with multiple psammoma bodies. Immunohistochemical examination showed that the tumor cells stained for somatostatin. Genomic examination showed neither K-ras nor p53 gene mutations of the resected specimen. [ABSTRACT FROM AUTHOR]
- Published
- 1996
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