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Introduction: Granular cell tumor (GCT) is a rare clinical entity derived from Schwann cells of the outer sheath of the peripheral nerves, involving skin and subcutaneous tissue in most cases, but specifically GCT of the vulva is less frequent and labium majus is more prevalent site in vulva. The exact prevalence and pathogenesis of GCT haven’t been determined, but the risk of malignancy has been described at the rate of 2%. The authors report a case of 52-year-old postmenopausal woman, with a 2-year slow growth vulvar mass, without associated symptoms. On physical examination, a hard consistent and nodular subcutaneous mass, with 5 cm and located over the mons pubis was observed. Pelvic magnetic resonance identified a solid mass with irregular borders on subcutaneous tissue, upon mons pubis. An aspiration cytology was performed, suggesting a GCT leading a complete excision. Microscopically, GCT was compatible with a GCT without malignancy characteristics and the margins were negative. Conclusion: This case reports a GCT on the mons pubis, whose rare location have only been reported in three cases. Despites its benign behavior, the unusual size conditioned a more aggressive surgical treatment and a multidisciplinary approach. During follow-up vulva and other anatomical locations should be carefully observed, because of its unusual local or extragenital recurrence.