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Introduction: Macular edema is a very rare complication of scleral necrosis after scleral buckling surgery., Observation: We report the case of a 45-year-old women with an ocular history of severe myopia in both eyes and retinal detachment in the left eye. She underwent segmental scleral buckling in 2003. Two years and nine months later, the patient had acute, painless visual loss in her left eye. Funduscopic examination revealed cystoid macular edema with no intraocular inflammation. A fluorescein angiography and OCT revealing cystoid macular edema consistent with the macular edema was noted clinically. The surgical exploration revealed scleral necrosis beneath the scleral buckle. After removal of the scleral buckle, a scleral patch was performed. Several months after surgery, the vision had improved; funduscopic examination and OCT revealed no residual macular thickening., Discussion: Macular edema is a rare complication of scleral necrosis following scleral buckling surgery, with only one case described in the literature. Our patient's complication occurred 2 years after surgery. The macular edema is likely the result of the scleritis. This inflammatory process can extend from the sclera and result in several ocular complications, including uveitis. Regression of macular edema occurs frequently after removal of the scleral buckle.

Ocular amyloidosis is infrequent, and the palpebral location is uncommon. It usually has a primary localized form, but can occur in systemic or familial amyloidosis. The diagnosis is mainly made by histopathology. Its treatment is surgical and the prognosis depends on clinical presentation and recurrences. We report the case of a 54-year-old woman with no medical history of the disease, who had bilateral isolated palpebral amyloidosis presenting as bilateral upper lid swelling with ptosis and corneal dystrophy. Diagnosis was confirmed by palpebral biopsy and the patient underwent excision of the involved lid tissue with reconstruction of the affected lid with cartilage autograft. Clinical progression showed improvement of the ptosis and the patient's comfort. Although rare, palpebral amyloidosis poses management problems, particularly in advanced cases, because of corneal complications and recurrence.

Primitive neuroectodermal tumor (PNET) of the orbit is rare. We present a case of a young patient with orbital PNET extending to the endo-crane and sinuses, which had been treated 10 years before with the diagnosis of rhabdomyosarcoma. The diagnosis was corrected with immunohistochemistry. Through this observation, we discuss the clinical aspects, the diagnosis difficulties, and the therapeutic options of this rare affection.

Introduction: Aniridia is a rare familial or sporadic disorder affecting not only the iris but also the cornea, angle structures, lens, optic nerve, and fovea. This disorder may be associated with many other systemic abnormalities such as urogenital malignancies., Case Reports: A 44-Year-old man who complained of visual loss presented bilateral congenital aniridia with corneal dystrophy and dense cataract. His 12-Year-old daughter also presented visual loss with severe bilateral corneal dystrophy and total congenital cataract associated with aniridia. Two other daughters, 18 and 23 Years of age, and an 11-Year-old son had nystagmus with bilateral congenital cataract and ectopia lentis. Clinical and radiological investigations did not disclose evidence of extraocular abnormalities in this family. Three patients underwent cataract extraction without intraocular implantation and the aphakia was corrected with glasses. All three patients progressed well., Discussion: This family provided a good illustration of the different clinical spectra of ocular involvement in congenital aniridia and its management difficulties, above all those of cataract surgery and correction of aphakia., Conclusion: Aniridia is a genetic disease with possible association with other ocular and systemic disorders, which may compromise visual and vital prognosis. Genetic advice is very important in such families.

A 26 year-old woman, whose parents were consanguineously married, was admitted to our center because of bilateral juvenile cataract. The patient exhibited short stature, sclerodermalike appearance of the skin with a typical bird-like facies, thinning and graying of hair, high pitched voice and hypogonadism. Werner's syndrome, was diagnosed. History, pathogeny, clinical features, diagnosis and cataract surgery are discussed.