1. Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review
- Author
-
Sami Ben Rhouma, Wissem Ben Mansoura, Habiba Mizouni, Seifeddine Boukriba, Alia Zehani, and Myriam Jrad
- Subjects
Spontaneous rupture ,medicine.medical_specialty ,Urology ,030232 urology & nephrology ,Wunderlich syndrom ,lcsh:RC870-923 ,03 medical and health sciences ,Tuberous sclerosis ,0302 clinical medicine ,Comparable size ,Female patient ,Medicine ,Hematuria ,Radical nephrectomy ,business.industry ,Unilateral nephrectomy ,medicine.disease ,lcsh:Diseases of the genitourinary system. Urology ,Oncology ,030220 oncology & carcinogenesis ,Shock (circulatory) ,Radiology ,medicine.symptom ,Giant angiomyolipoma ,business ,Renal angiomyolipoma ,Hemodynamic instability - Abstract
Enormous bilateral renal angiomyolipoma (AML) are extremely rare, their spontaneous bleeding also called Wunderlich's syndrom (WS) is also an unusual situation.It is considered as a life threatening condition requiring fast and effective care.We present a case of hypovolemic shock due to spontaneous rupture of bilateral giant angiomyolipomas in a 35-year-old female patient with tuberous sclerosis complex (TSC).The hemodynamic instability of the patient leads to an immediate surgery and unilateral nephrectomy was done for the biggest angiomyolipomas. The review of the literature revealed only few cases of spontaneous rupture of renal angiomyolipomas of comparable size. Keywords: Wunderlich syndrom, Hematuria, Radical nephrectomy, Giant angiomyolipoma
- Published
- 2020