1. [Muscular haematoma in Henoch-Schönlein purpura].
- Author
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Mahevas M, Makdassi R, Presne C, Bernasconi T, Cordonnier C, Fournier A, and Choukroun G
- Subjects
- Aged, Humans, Male, Severity of Illness Index, Hematoma etiology, IgA Vasculitis complications, Muscular Diseases etiology
- Abstract
Introduction: Henoch-Schonlein purpura is one of the most frequent systemic vasculitis in children. In adults, muscle involvement is extremely rare and not very well characterized. We report a case of Henoch-Schonlein purpura with severe skin and renal involvement in witch multiple intramuscular haematoma leaded to severe anaemia. Histological examination confirms the muscle localization of the disease., Exegesis: A 68 years old man treated by oral anticoagulation for multiple venous thrombosis, was admitted with necrotic vasculitis of the skin, abdominal pain and segmental IgA glomerulopathy. The diagnosis of Henoch-Schonlein purpura was rapidly made and intensive steroid therapy started. After rapid improvement, a haemorrhagic shock due to voluminous intramuscular haematoma was diagnosed by MRI. Histological examination of the muscle, confirms the localization of the disease., Conclusion: Intramuscular haematomas are very uncommon in Henoch-Schonlein purpura. There are usually a consequence of muscular immune complex vasculitis. In our patient, high dose corticosteroid was not unable to control the disease.
- Published
- 2004
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