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Objectives: To summarize the clinical features, diagnosis, treatment strategies, and prognosis of alveolar soft part sarcoma (ASPS) of the oral and maxillofacial region., Study Design: We performed a retrospective study in a consecutive series of 18 patients with ASPS of the oral and maxillofacial region between 1995 and 2013. Demographic characteristics, tumor sizes, sites, tumor metastasis, diagnosis, treatments, and overall follow-ups were documented., Results: The 18 patients were diagnosed pathologically with primary tumor developed on the tongue (10), the cheek (5), the pharynx (1), and the gingiva (2) with an average tumor size of 4 cm. At the latest follow-up, 1 patient with lung metastases survived for 23 months; 1 died 3 months after the confirmation of local recurrence and multiple pulmonary metastases; the rest of the patients were disease free and remained in good health., Conclusions: ASPS of the oral and maxillofacial region appears to have special clinical characteristics., (Copyright © 2015. Published by Elsevier Inc.)

Objective: We report a case of alveolar soft part sarcoma (ASPS) of the tongue that presented in the third trimester of pregnancy., Case Report: An 18-year-old, gravida 1, para 0, woman with ASPS of the tongue in the 31st week of pregnancy was described. Approximately 4 months after her first diagnosis, she was referred to our clinic for the delivery of her baby and additional treatment. At 32 weeks of gestation, a healthy male infant weighing 2,220 g was delivered by cesarean section. After an uneventful postoperative course, she was referred to the department of otorhinolaryngology and maxillofacial surgery for further investigation and treatment., Conclusion: ASPS of the tongue presenting in pregnancy is an extremely rare combination, and to our knowledge, this is the first reported case in the English literature. The diagnostic and therapeutic management of the pregnant patient with cancer, like ASPS, is especially difficult, because it involves both the mother and fetus.