1. Pneumoblastoma in neurofibromatosis.
- Author
-
Bron LP, Howarth NR, and Muller AF
- Subjects
- Adult, Humans, Male, Radiography, Lung Neoplasms diagnosis, Lung Neoplasms diagnostic imaging, Neoplasms, Multiple Primary diagnosis, Neoplasms, Multiple Primary diagnostic imaging, Neurofibromatoses
- Abstract
Pneumoblastoma is a rare tumor composed of two histologic cell types, arising from epithelium and stroma. Patients with von Recklinghausen's disease are known to develop certain types of tumors. A rare, and possibly first case of pneumoblastoma arising in a patient with neurofibromatosis is described.
- Published
- 1993
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