1. Coronary periarteritis in a patient with multi-organ IgG4-related disease.
- Author
-
Guo Y, Ansdell D, Brouha S, and Yen A
- Subjects
- Aged, 80 and over, Anti-Inflammatory Agents therapeutic use, Diagnosis, Differential, Glucocorticoids therapeutic use, Heart diagnostic imaging, Humans, Hypergammaglobulinemia diagnostic imaging, Hypergammaglobulinemia drug therapy, Male, Pericarditis diagnostic imaging, Pericarditis drug therapy, Prednisone therapeutic use, Tomography, X-Ray Computed, Treatment Outcome, Hypergammaglobulinemia immunology, Immunoglobulin G immunology, Pericarditis immunology
- Abstract
Immunoglobulin G4-related disease is a recently described systemic clinicopathological entity characterized by immunoglobulin G4-producing plasmacytic infiltration of tissue and frequently by elevated serum immunoglobulin G4 concentration. Manifestations of this disease have been documented in nearly all organs and locations, but coronary artery involvement is not widely recognized. We report the coronary findings of a patient with multi-organ immunoglobulin G4-related disease. Non-electrocardiogram-gated computed tomography of the chest demonstrated nodular and rind-like periarterial soft tissue thickening along the proximal coronary artery segments with improvement following steroid therapy.
- Published
- 2015
- Full Text
- View/download PDF