1. A rare case of kartagener’s syndrome [Nadir görülen kartagener sendromlu bir olgu]
- Author
-
Elverişli, Mehmet Fatih, Gülhan, Pınar Yıldız, Yıldız, Şule, and Balbay, Ege Güleç
- Subjects
Kartagener syndrome ,Obstructive sleep apnea ,Primary ciliary dyskinesia - Abstract
Kartagener syndrome is a rare autosomal recessive disorder seen about in one per 30000 live births and characterized by bronchiectasis, chronic sinusitis and situs inversus triad. Absence of dynein arms in epithelial cilia is the most common defect in electron microscopic examination. Extreme sputum retention is seen due to cilial disfunction in this disease. Treatment of the disease is directed to symptoms. Infertility and deafness can be seen. It has been also observed that Kartagener syndrome decreases sleep quality. In order to protect the patients from infections, chest physiotherapy, influenza and pneumococcal vaccines are recommended. These patients should stay away from particulate included gases such as dust and smoke. In this study, a 33 year old male patient diagnosed late despite frequent hospital admissions, coexistence with obstructive sleep apnea syndrome was presented with clinical and radiological findings. © 2019, Duzce University Medical School. All rights reserved.
- Published
- 2019