1. Severe Outcome of Pharyngeal-Cervical-Brachial Pure Motor Axonal Neuropathy
- Author
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Laura Bonanni, Astrid Thomas, V. Scorrano, V. Onofrj, and Marco Onofrj
- Subjects
Denervation ,medicine.medical_specialty ,business.industry ,Article ,Surgery ,Psychiatry and Mental health ,Lower body ,medicine.anatomical_structure ,Motor axonal neuropathy ,Neurology ,Muscle action ,Normal reflexes ,Anesthesia ,Medicine ,Neurology (clinical) ,business ,Sensory nerve - Abstract
We present two further cases of the pharyngeal-cervical-brachial (PCB) form of GBS, with unfavourable outcome, showing dramatic dissociation between upper and lower body Symptoms. Both patients showed rapidly progressive motor denervation with disappearance of Compound Muscle Action Potentials (CMAPs) in upper limbs muscles. Sensory Nerve Action Potentials (SNAPs) were instead normal. Normal reflexes, F waves and action potentials were elicited in lower limbs. Despite i.v. Immunoglobulin treatment no recovery was observed and both patients died within a year from onset of symptoms.
- Published
- 2010
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