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Absent left pulmonary artery with Tetralogy of Fallot (TOF) with absent pulmonary valve syndrome (APVS), is a rare congenital cardiac anomaly. Here we present such a case of A 2 year 11 month old girl with cyanosis, exertional dyspnoea. Her diagnosis is confirmed by echocardiography and CT angiogram. There are very few cases have been reported till date with high postoperative mortality. Although per operative decision making was challenging regarding pulmonary valve and size of the RPA, we performed ICR with RPA reductionplasty and creation of monocuspid pulmonary valve with success. As it is a rare association and we have overcome the hindrance we came across per operatively, we are reporting this case. Bangladesh Heart Journal 2020; 35(1) : 74-77

24 year old young lady came to us with a diagnosis of atrial septal defect (ASD) secundum who lost her follow up since her 4 years of age. Later her history, physical findings and investigations change the diagnosis into supracardiac total anomalous pulmonary venous drainage. Typical ‘snowman sign’ in chest x-ray and transthoracic echo helped to review the case. Proper history taking and careful evaluation by investigation is needful for each individual. Cardiovasc. j. 2019; 12(1): 75-78

Objective: To identify the incidence and related factors for pulmonary complications and its impact on outcome in patients subjected to surgery for congenital heart disease (CHD).Methods: The sample comprised 141 patients of both genders, subjected to surgery for CHD, during 3 months period from 1st July 2014 to 30th September 2014. The data were obtained from newly improvised Congenital Heart Surgery Database.Results: Twenty eight (20%) patients developed some form of pulmonary complications. Age, weight, length and body surface area are significantly low among them (p

A 2 years old boy presented to us with a history of repeated respiratory tract infections and bluish discoloration of tongue, lips and figure tips for last 18 months. Echocardiography and Computed tomography (CT) angiogram revealed total anomalous pulmonary venous connection (TAPVC) mixed type (supracardiac and cardiac);all pulmonary veins drain into a common chamber behind left atrium (LA) and left lower pulmonary vein (LUPV) drains to vertical vein and common chamber both.The patient underwent rerouting of pulmonary veins and vertical vein ligation above the drainage of LUPV. Bangladesh Heart Journal 2018; 33(2) : 138-140