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Infantile myofibromatosis (IM) is the most common fibrous disorder of infancy and early childhood. Solitary intracranial involvement is rare and often unrecognized. This makes its early diagnosis and adequate management difficult. The majority of lesions are localized to the skull or dura with variable intracranial extension. Herein, we report a misdiagnosed and aggressive presentation of a solitary IM of the petrous bone. Our aim is to discuss histopathological differential diagnoses and management difficulties.

Renal cell carcinomas are tumors known for their metastatic potential. The lungs, the lymph nodes, the lungs, the spleen, the adrenal gland and the cervix remain the metastatic sites of predisposition. The symptoms of metastatic lesion may be due to the initial manifestation of renal malignancy. We report in this work a buccal localization of metastases from renal cell carcinoma to clear cells in a patient aged 65 years or less in our department of otolaryngology and cervical-facial surgery.

Frontal sinuses that present with abnormally large size are often clinically described as a deformity of the forehead, caused by Pneumosinus dilatans (PD). We report a rare case of Pneumosinus dilatans frontalis which was accidentally discovered by a paranasal sinus CT scan requested following frontal headaches, and thus revealing diffuse osteoporosis. Pneumosinus dilatans is often an unexpected radiological finding; however, in most cases, it is diagnosed by recognition of a frontal deformity.

Paraganglioma is a rare neuroendocrine tumor. Nasal localization is very rare. Head and neck paragangliomas represent only 0.6% of head and neck tumors and 3% of all paragangliomas. The treatment is based on surgery. Radiotherapy is indicated if the surgery does not provide complete resection. We report the case of a 36-year-old patient who has had left nasal obstruction with epistaxis for 2 years. The CT scan shows a solid mass centered on the left nasal cavity, puffy, without signs of aggression, benign-looking. The patient underwent a complete endoscopic endonasal tumor removal after preoperative external carotid embolization. Pathological analysis with immunohistochemistry confirmed the diagnosis of paraganglioma. The follow-up to the treatment was favorable.

La myiase est une maladie causee par les larves de mouches. La localisation auriculaire (otomyiase) est une affection rare, causee frequemment par les especes de la famille des sarcophages. Elle survient souvent sur des lesions chroniques negligees chez des personnes dont l´hygiene est precaire. Depuis longtemps au Maroc la myiase a ete decrite. Cependant, peu d´etudes epidemiologiques ont ete consacrees a cette affection. Nous rapportons dans ce travail l´observation de deux patientes recues et prises en charge aux Urgences d´Oto-rhino-laryngologie et de Chirurgie Cervico-faciale a l´Hopital des Specialites (CHIS), Rabat, Maroc.

Le syndrome de Lemierre « SL » est une maladie rare qui prend son origine tres souvent d´une infection oropharyngee se compliquant d´une thrombose septique de la veine jugulaire interne et d´emboles septiques a predominance pulmonaire dans sa forme typique. Dans notre cas, le SL n´est qu´un tableau revelateur d´un carcinome epidermoide de la bouche œsophagienne surinfecte. Tout retard diagnostic ou de prise en charge peut etre responsable d´une morbi-mortalite elevee. Son diagnostic repose sur : un faisceau d´arguments cliniques, radiologiques dont la TDM cervico thoracique avec injection du produit de contraste trouve tout son interet ainsi que sur des examens bacteriologiques surtout dans les formes atypiques. Le traitement est principalement medical base sur une antibiotherapie ciblee urgente et prolongee, l´anticoagulation reste tres discutee cas par cas, et le traitement chirurgical est reserve a des cas bien particuliers.

Kikuchi-Fujimoto's disease KFD is a rare and benign cause of cervical lymphadenopathy. It is an anatomoclinical entity of unknown etiology. The confirmation of the diagnosis is always provided by histological lymph node study. The clinical picture sometimes evokes lymphoma or tuberculosis. The evolution is generally favorable with spontaneous healing after a few weeks. We report the case of a 26-year-old woman who had consulted for cervical lymphadenopathy associated with fever. The cervical lymph node biopsy concluded to Kikuch-Fujimoto's disease. The evolution was marked by rapid regression of lymphadenopathy under corticosteroid treatment.

Rhinolithiasis is a rare condition often neglected or unknown that tends to disappear in developed countries and corresponds to a solid calcification by gradual deposition of calcareous salts around a central resorbable or non-resorbable foundation of varying shape and size. The most common symptom is a long-term unilateral purulent rhinorrhea and unilateral nasal obstruction. Nasal endoscopy and imaging are interesting for the positive diagnosis but especially to highlight the anatomical anomalies or related pathologies. Therapeutic management requires endonasal extraction of the rhinolith under general anesthesia. We report an observation of rhinolithiasis treated in our department associating a significant deformation of the nasal pyramid to osteolysis.

Kartagener syndrome is an autosomal recessive genetic ciliary disorder comprising of a classic triad of sinusitis, situs inversus and bronchiectasis. It's the one of primary ciliary dyskinesia disorders with manifestations present from childhood. Most patients of PCD have situs inversus. We present a case of 18 year-old women with recurrent lower and upper respiratory tracts infections, and rhinolalia clausa.Pan African Medical Journal 2016; 23