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The congenital long QT syndrome (LQTS) is considered to be one of the hereditary cardiac arrhythmia syndromes, nowadays also known as cardiac channelopathies. The syndrome is characterized by prolongation of the heart rate corrected QT-interval (QTc) on the 12-lead electrocardiogram (ECG). In affected family members, it is associated with recurrent syncope, seizures, and sudden cardiac death due to ventricular arrhythmias (Torsade des Pointes (TdP) and ventricular fibrillation), which typically follow a precipitating event such as exertion, extreme emotion, swimming and diving, or auditory stimulation. [ABSTRACT FROM AUTHOR]