1. Aortic microcalcification is associated with elastin fragmentation in Marfan syndrome
- Author
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Wanga, Shaynah, Hibender, Stijntje, Ridwan, Yanto, van Roomen, Cindy, Vos, Mariska, van der Made, Ingeborg, van Vliet, Nicole, Franken, Romy, van Riel, Luigi Amjg, Groenink, Maarten, Zwinderman, Aeilko H., Mulder, Barbara Jm, de Vries, Carlie Jm, Essers, Jeroen, de Waard, Vivian, Molecular Genetics, Radiotherapy, Graduate School, Other departments, AGEM - Amsterdam Gastroenterology Endocrinology Metabolism, Medical Biochemistry, ACS - Amsterdam Cardiovascular Sciences, Cardiology, APH - Methodology, Epidemiology and Data Science, APH - Personalized Medicine, APH - Aging & Later Life, ACS - Heart failure & arrhythmias, ACS - Diabetes & metabolism, and ACS - Atherosclerosis & ischemic syndromes
- Subjects
cardiovascular system ,macromolecular substances - Abstract
Marfan syndrome (MFS) is a connective tissue disorder in which aortic rupture is the major cause of death. MFS patients with an aortic diameter below the advised limit for prophylactic surgery (
- Published
- 2017