1. Bleeding symptoms and laboratory correlation in patients with severe von Willebrand disease
- Author
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Angela Lambing, Mary G. Hudson, Deanna Mitchell, Angela Tackney, Michael Recht, Erica Johnson, Ray L. Watts, Adam Cuker, JeanMarie M. Zoland, Karen Gutting, Cherys Zimmerman, Ellen White, Glenda Eckert, Gita Massey, Elizabeth Sandon-Kleiboer, Steve Hopewell, Trish Underland, Leslie Witkoff, Angie Riedel, Susan Karp, Cheryl Brower, Kathy McGinty, Charles Sexauer, Glenn Heggie, Joanne Porter, Mark T. Reding, Susumu Inoue, Vivek R. Sharma, Ashley T. Brummel, Marion Koerper, Sarah May, Jonathan M. Ducore, John S. Rogers, Claudia Lupia, C. Wang, Sue Geraghty, Eric H. Kraut, Neiha Dhar, Eric J. Werner, Bertil Glader, Margaret Bosch, Bryce A. Kerlin, Jodi Haar, Roberto Torres, Hassan M. Yaish, Mia Frank, Jay Charles, Jeanne M. Lusher, Dominique Joseph, Philip Kuriakose, Paula L. Bockenstedt, JoAnn A. Ruff, Mary Catherine Noa, Amy E. Lovejoy, Anaadriana Zakarija, Ilene Goldberg, Donna DiMichele, Anne T. Neff, Miriam Granat, Edwin N. Forman, Robin Schwartz, Alice Cohen, Margaret V. Ragni, Brian M. Wicklund, Michael F. Guerrera, Joan Cox Gill, Nadia P. Ewing, Ulrike M. Reiss, Kimo C. Stine, Sue Kovats-Bell, Robin Grant, Tom Coyle, Felicia Kiplinger, Thomas C. Abshire, Desiree Medeiros, Franklin Desposito, Katie Kralovetz, William D. Haire, Paulette Drozdowicz, Michael D. Tarantino, Rosemary P. Holmberg, Angela Stewart, Peter A. Kouides, Jennifer Green, Amy D. Shapiro, Karen Panckeri, Jim Casella, Guy Young, Sylvia Webber, Lee Meadows, Sandy Hibner, Katherine Farrow, Ara Metjian, Cecilia V. Schmidt, Laura Schulz, Robert Mignacca, S. M. Peterson, Sandy Harris, Parvin Saidi, W. Keith Hoots, Hernan Sabio, Diana Mathis, Kenneth D. Herbst, Cathy Glass, Jorge DiPaola, Patricia Fleming, Lisa Palumbo, Richard Lipton, Kristen Jaworski, Valerie Gonzalez, Valerie Crenshaw, Kim Stewart, Craig M. Kessler, Dee Ann Omatsu, Wahid Hanna, Patricia Amerson, Alexis A. Thompson, Afshin Ameri, Helena M. Jacobs, James French, Anne Chambers, Marjorie A. Boyd, George R. Buchanan, Steven W. Pipe, Anita Smith, Jubelirer Sj, Karen Granger, K. A. Schmidt, Suman L. Sood, Becki Berkowitz, Cindy A. Leissinger, Rajiv K. Pruthi, Patricia Ashby, Susan Curoe, Brenda Nielsen, Amy L. Dunn, Mike Lammer, Donna Arden, Carol Diamond, Chris Guelcher, Frances Patterson, Arthur R. Thompson, M. E. Nolte, G. Allen, Alan C. Homans, Marilyn J. Manco-Johnson, Ralph A. Gruppo, Glen Roy, Vlad C. Radulescu, Elizabeth Hanlon, Lynn Menza, Sarah Alexander, J. M. Soucie, Nigel S. Key, Debbie Nelson, Lisa Pullens, Jennifer La Franco, Barbara A. Konkle, Jean Marandola, Jonathan Bernstein, Muriel Herr, and Corinthian Bryant
- Subjects
Male ,congenital, hereditary, and neonatal diseases and abnormalities ,medicine.medical_specialty ,Adolescent ,Genotype ,Population ,Hemorrhage ,Gastroenterology ,Severity of Illness Index ,Young Adult ,Von Willebrand factor ,hemic and lymphatic diseases ,Internal medicine ,Arthropathy ,Severity of illness ,Hemarthrosis ,von Willebrand Factor ,medicine ,Von Willebrand disease ,Humans ,Young adult ,education ,Child ,Genetics (clinical) ,education.field_of_study ,biology ,business.industry ,Clinical Laboratory Techniques ,Hematology ,General Medicine ,Bleed ,medicine.disease ,United States ,Surgery ,von Willebrand Diseases ,Child, Preschool ,biology.protein ,Female ,business ,Body mass index - Abstract
Type 3 von Willebrand disease (VWD) is a rare bleeding disorder with markedly decreased or absent von Willebrand factor (VWF) protein, accompanied by a parallel decrease in VWF function and factor VIII (FVIII) activity. The goal of this study was to describe the population of patients enrolled in the USA Centers for Disease Control Universal Data Collection (UDC) study with type 3 VWD, defined as a VWF:Ag of
- Published
- 2009