1. Síndrome de Kinsbourne: revisión de nuestra casuística
- Author
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Martínez-Antón J, Rodríguez-Barrionuevo Ac, Delgado-Marqués Mp, Caballero-Morales Ma, and Mora-Ramírez
- Subjects
Pediatrics ,medicine.medical_specialty ,Cerebellar ataxia ,business.industry ,Incidence (epidemiology) ,Retrospective cohort study ,General Medicine ,Disease ,Opsoclonus ,medicine.disease ,Kinsbourne Syndrome ,Neuroblastoma ,medicine ,Neurology (clinical) ,Presentation (obstetrics) ,medicine.symptom ,business - Abstract
INTRODUCTION The childhood opsoclonus-myoclonus or Kinsbourne syndrome, is a uncommon process, of acute or subacute beginning, which affects infant and children. It's course is characterized by opsoclonus, polimyoclonias and cerebellar ataxia. The disease is frequently associated to neuroblastoma (46%). MATERIAL AND METHODS We present a retrospective study on 9 patients, emphasizing the clinical presentation and the evolution aspects. RESULTS AND CONCLUSIONS We found changes in the EEG in three cases. Most surprising is the scarce incidence of neuroblastoma, which has been found only in a one out of nine patients. We found three cases with relapse during the treatment or on withdrawal and one of them relapsed twice again. The evolution has been variable, since 5/9 patient have presented some type of mild or moderate neuro-psychological sequelae. Out of three patient with relapses, two presented permanent neurological sequelae. A patient which suffered three relapses, is also the one which presents more serious sequelae.
- Published
- 1998
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