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Desmoid tumor is an uncommon form of fibromatosis of extremely rare musculoaponeurotic origin. Most are located in the abdomen, and its location in the chest wall is very rare. Due to its inability to produce metastases it has been considered benign, however, its rapid and aggressive local growth makes the surgical treatment equally aggressive and complete. We present a case of a thoracic wall desmoid tumor in a 40-year-old patient, one year evolution, with rapid and aggressive growth which deforms the anatomy of the thoracic wall. Excision of the tumor and 5 partially costal arches were performed, with subsequent thoracic reconstruction with prosthetic material and dermo-fat flap. Desmoid tumors, in advanced stages, requires multidisciplinary participation. [ABSTRACT FROM AUTHOR]

Copyright of Cirugía y Cirujanos is the property of Publicidad Permanyer SLU and its content may not be copied or emailed to multiple sites or posted to a listserv without the copyright holder's express written permission. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract. (Copyright applies to all Abstracts.)

Copyright of Cirugía y Cirujanos is the property of Publicidad Permanyer SLU and its content may not be copied or emailed to multiple sites or posted to a listserv without the copyright holder's express written permission. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract. (Copyright applies to all Abstracts.)

Copyright of Salud Uninorte is the property of Fundacion Universidad del Norte and its content may not be copied or emailed to multiple sites or posted to a listserv without the copyright holder's express written permission. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract. (Copyright applies to all Abstracts.)

Background: Patients with classic familial adenomatous polyposis syndrome (FAPc) have a germline mutation in the APC gene. The most common phenotypic expression is the presence of multiple colorectal adenomatous polyps (more than 100), with high probability developing colorrectal cancer (CRC) before the fifth decade of life. Prophylactic surgery (total colectomy or restorative proctocolectomy) reduces the risk of developing CRC. However, the risk of developing tumors in other organs remains present. Objetive: Analyze the frequency and type of tumors associated with classic familial adenomatous polyposis syndrome (FAPc) patients undergoing prophylactic colectomy. Material and Methods: Cohort study. From the registry of hereditary colorrectal cancer (CRC) at our institution, we identified patients with FAPc who underwent total colectomy with ileorrectal anastomosis (TC-IRA) or restorative proctocolectomy (RTPC), from 1999 to 2014. In the follow-up we analyzed related tumors and mortality. Results: 27 patients, of whom 18 (66.7%) underwent TC-IRA and 9 (33.3%) underwent RTPC. At the time of surgery, 4 patients had CRC (15%) and 5 had extracolonic tumors (osteomas). In a mean follow-up of 49, 4 months (i: 2 y 178) the following lesions were diagnosed: digestive tract adenomas in 17 (63%) patients, of these 2 required a proctectomy and 3 resection of duodenal adenomas. Eight patients developed desmoid tumors (30%), and 3 of them underwent surgery. One patient had an extradigestive tumor (thyroid cancer) and only 8/27 (29.6%) did not develop other tumors. One patient died due to progression of his CCR. Discussion: In this series it is confirmed that most patients will develop neoplasms FAPc after colectomy. Conclusion: The removal of the colon and/or rectum is able to prevent the development of CRC. However, two thirds of the patients develop other tumors in which systematic surveillance allowed early detection and treatment. [ABSTRACT FROM AUTHOR]

The desmoid tumor also known as muscle-aponeurotic fibromatosis, aggressive fibromatosis, deep fibromatosis, no metastatic fibrosarcoma and fibrosarcoma grade I, is an aggressive fibromatosis of slow and gradual installation .There are discrepancies regarding optimal treatment; because of its benign nature surgery is justified, but in some cases, chemotherapy has been administered, when evolution is not the usual and has existed response to this medication. Desmoid tumors can be considered as sarcomas with very low virulence. Conventional wisdom would indicate that such tumors would not have any response to chemotherapy, but the opposite happens. It has an incidence of 3-4 cases per million, with a peak between 25 and 35 years of age, affecting mainly females. Presents high probability of recurrence. It usually occurs in women in the postpartum period, the rectus abdominis and the scars of abdominal surgery. But can appear in any muscle. We present the case of a female aged 27 with APP health until November 2010 when she was diagnosed with left renal calculi and subjected to partial nephrectomy lumbotomy. One year and nine months after, having eight weeks of pregnancy, in the area of the scar a tumor appears. The tumor had rapid growth hard consistency without being painful, after diagnostic procedures, it was concluded as a desmoid tumor, expressing their diagnosis and treatment, the case was diagnosed in the Camilo Cienfuegos Hospital of Sancti Spiritus Cuba. [ABSTRACT FROM AUTHOR]

Mammary fibromatosis or desmoid tumor is a rare lesion which accounts for less than 0.2% of all mammary tumors. It represents a proliferation of fibroblasts, myofibroblasts, or both, which infiltrate the stroma of the breast locally and aggressively but without potential to cause metastasis. The causes are unknown; however, there is a clear association with a history of traumatism and breast surgery (e.g. tumorectomy, reductive surgery, or placement of implants). The clinical and image presentations imitate, almost undistinguishably, an invasive carcinoma. The diagnosis is histological and the treatment of choice is full surgical resection, due to the tumor's high rate of local recurrence, even with free surgical margins. [ABSTRACT FROM AUTHOR]

Copyright of Cirugía y Cirujanos is the property of Publicidad Permanyer SLU and its content may not be copied or emailed to multiple sites or posted to a listserv without the copyright holder's express written permission. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract. (Copyright applies to all Abstracts.)

Copyright of Cirugía y Cirujanos is the property of Publicidad Permanyer SLU and its content may not be copied or emailed to multiple sites or posted to a listserv without the copyright holder's express written permission. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract. (Copyright applies to all Abstracts.)

Desmoid tumours are locally aggressive tumours without metastasic potential which generally can be treated with local treatments such as surgery or radiotherapy. Systemic therapy also can be considered. Anyway there is an unpredictable pathology that will need a careful and personal clinic evaluation to choose the most suitable treatment. We report a case of a patient diagnosed of retroperitoneal desmoid tumour. [ABSTRACT FROM AUTHOR]