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OBJECTIVE: To describe our experience in the cardiovascular characteristics and clinical evolution of patients with MS, ED and LD. MATERIALS AND METHODS: Patient records from the last 10 years were reviewed in a cross-sectional, observational and retrospective study. The diagnosis was made with family history and Ghent clinical criteria. Cardiac characteristics, treatment and clinical criteria. Cardiac characteristics, treatment and clinical behavior were analyzed. Percentages and frequencies are made. RESULTS: Thirty patients with SM, 18 with ED and 3 with LD (51 patients) were studied. The male gender predominated and the age ranged between 1 and 17 years of age. Patients with SM had 50% of family history, with LD 66% and with ED 44%. Cardiovascular alterations occurred in patients with MS in 73%, the most frequent being dilation of the aortic root. 66.6% patients with LD had vascular disease. Treatment was based on losartan and propranolol. None were managed with cardiovascular surgery. Follow-up ranged from 6 months to 9 years. The majority had no cardiovascular symptoms. None died. CONCLUSIONS: In patients with SM and LD, cardiovascular disease is common in children and adolescents. It is advisable to continue cardiovascular monitoring and early treatment. [ABSTRACT FROM AUTHOR]

The case report of a 29 year-old patient, with a history of aortic ectasia who had been studied when she was 18 years through cineangiography is presented and a fusiform aneurysm of the infrarrenal abdominal aorta and of the left primitive iliac artery, of unspecific cause was found, which were substituted with left aortofemoral bypass. Later on, in 2012, she presented pain and increase of the volume in the left inguinal region, reason why she was assisted in the emergency room of "Saturnino Lora Torres" Teaching Provincial Clinical Surgical Hospital in Santiago de Cuba, and evaluated by specialists of the Angiology and Vascular Surgery Service, which determined to treat her with an emergency surgery, when observing an anastomotic aneurysm of the left femoral artery of fungal cause, and the characteristics: craneosinostosis, bifid uvula and cleft palate; characteristic of Loeys Dietz syndrome. [ABSTRACT FROM AUTHOR]