1. [Mayer-Rokitansky-Küster-Hauser syndrome. A report of two cases].
- Author
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Bautista-Gómez E, Morales-García V, Galván Espinosa H, Flores-Romero AL, Vásquez Santiago E, and Pizarro Osorno N
- Subjects
- 46, XX Disorders of Sex Development, Abnormalities, Multiple diagnostic imaging, Abnormalities, Multiple embryology, Abnormalities, Multiple epidemiology, Abnormalities, Multiple surgery, Adolescent, Adult, Congenital Abnormalities, Endometriosis etiology, Female, Humans, Hysterectomy, Incidence, Kidney abnormalities, Kidney diagnostic imaging, Kidney embryology, Kidney pathology, Kidney surgery, Mullerian Ducts abnormalities, Mullerian Ducts diagnostic imaging, Mullerian Ducts embryology, Mullerian Ducts pathology, Mullerian Ducts surgery, Pelvic Pain etiology, Phenotype, Somites abnormalities, Somites diagnostic imaging, Somites embryology, Somites pathology, Somites surgery, Spine abnormalities, Spine diagnostic imaging, Spine embryology, Spine pathology, Spine surgery, Surgically-Created Structures, Ultrasonography, Uterus abnormalities, Uterus diagnostic imaging, Uterus embryology, Uterus pathology, Uterus surgery, Vagina abnormalities, Vagina diagnostic imaging, Vagina embryology, Vagina pathology, Vagina surgery, Abnormalities, Multiple pathology, Amenorrhea etiology
- Abstract
The Mayer-Rokitansky-Kuster-Hauser is a rare congenital anomaly characterized by lack of vaginal and uterine development variable and normal ovaries. It results from agenesis or hypoplasia Müller duct system. Cervicovaginal agenesis as part of the complex syndrome, is even rarer. We report two cases: adolescent patient with primary amenorrhea, cervicovaginal agenesis and chronic pelvic pain, and a 28-year-old patient with primary amenorrhea, congenital absence of uterus and vagina.
- Published
- 2012