1. [Hereditary tylosis syndrome and esophagus cancer].
- Author
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de Souza CA, Santos Ada C, Santos Lda C, and Carneiro AL
- Subjects
- Adult, Female, Humans, Keratoderma, Palmoplantar, Diffuse genetics, Carcinoma, Squamous Cell complications, Esophageal Neoplasms complications, Keratoderma, Palmoplantar, Diffuse complications
- Abstract
Tylosis palmoplantaris is an autosomal dominant disorder characterized by hyperkeratosis of palms and soles. Lesions start during childhood and are more evident in areas of pressure. Familial tylosis palmoplantaris comprises two forms: epidermolytic and non-epidermolytic. Patients with the epidermolytic variant have up to 40% higher chance of developing squamous cell carcinoma of the esophagus. The association of tylosis palmoplantaris with esophageal cancer is called Howel-Evans syndrome.
- Published
- 2009
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