1. Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart.
- Author
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Leite LR, Ponzi Pereira KR, Alessi SR, and de Paola AA
- Subjects
- Adrenergic beta-Antagonists therapeutic use, Child, Electrocardiography, Female, Follow-Up Studies, Humans, Nadolol therapeutic use, Tachycardia, Ventricular diagnosis, Tachycardia, Ventricular drug therapy, Death, Sudden, Cardiac etiology, Syncope etiology, Tachycardia, Ventricular complications
- Abstract
Syncope in children is primarily related to vagal hyperreactivity, but ventricular tachycardia (VT) way rarely be seen. Catecholaminergic polymorphic VT is a rare entity that can occur in children without heart disease and with a normal QT interval, which may cause syncope and sudden cardiac death. In this report, we describe the clinical features, treatment, and clinical follow-up of three children with syncope associated with physical effort or emotion and catecholaminergic polymorphic VT. Symptoms were controlled with beta-blockers, but one patient died suddenly in the fourth year of follow-up. Despite the rare occurrence, catecholaminergic polymorphic VT is an important cause of syncope and sudden death in children with no identified heart disease and normal QT interval.
- Published
- 2001
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