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We present a case report of an eight-year-old patient with hypoplastic left heart syndrome (HLHS) after Fontan operation with the first onset of plastic bronchitis. Plastic bronchitis is one of the rare late complications of the Fontan procedure in patients with a univentricular heart, occured in 1-4% of Fontan patients. Hypoplastic left heart syndrome is one of the most complex congenital heart defects. It consists of hypoplasia of the left heart structures. In this malformation it is not possible to restore normal anatomical conditions. Plastic bronchitis is characterised by formation of bronchial casts leading to airway obstruction. Other symptoms are dyspnea, cyanosis, chronic cough, respiratory sounds asymmetry, deterioration of exercise tolerance. Those symptoms can suggest chronic infection, asthma or a foreign object in the airways which can delay and complicate the diagnostic process. [ABSTRACT FROM AUTHOR]