17 results on '"De Beuckeleer, LH"'
Search Results
2. Intracortical osteosarcoma: is MRI useful?
- Author
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Vanhoenacker F, De Beuckeleer LH, and De Schepper AM
- Subjects
- Adult, Diagnosis, Differential, Female, Humans, Image Enhancement, Sensitivity and Specificity, Bone Neoplasms diagnosis, Osteosarcoma diagnosis, Tibia pathology
- Published
- 2001
- Full Text
- View/download PDF
3. Low-grade chondrosarcoma vs enchondroma: challenges in diagnosis and management.
- Author
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Wang XL, De Beuckeleer LH, De Schepper AM, and Van Marck E
- Subjects
- Adult, Biopsy, Bone Neoplasms pathology, Diagnosis, Differential, Follow-Up Studies, Humans, Male, Thoracic Neoplasms pathology, Bone Neoplasms diagnosis, Chondroma diagnosis, Chondrosarcoma diagnosis, Magnetic Resonance Imaging, Ribs pathology, Thoracic Neoplasms diagnosis, Tomography, X-Ray Computed
- Abstract
A 28-year-old man presented with a swelling at the right thoracic wall. Computed tomography showed an aggressive process involving the cortex of the rib with concomitant soft tissue mass. However, a needle biopsy specimen revealed an enchondroma and consequently the physician decided to apply a "wait-and-see" strategy. After 3 years of careful follow-up by MR imaging, the patient complained of subtle enlargement of the lesion, which was later confirmed on repeated CT scan. Despite an aggressive appearance on control MR imaging, histopathological examination after incisional biopsy could not differentiate between enchondroma and low-grade chondrosarcoma. Wide excision including previous biopsy trajectory was performed. Diagnosis of a low-grade (grade I) chondrosarcoma was made on findings of the excisional specimen and seeding of cartilage tissue along the previous incisional biopsy trajectory was found.
- Published
- 2001
- Full Text
- View/download PDF
4. Thyroid acropachy: correlation of imaging and pathology.
- Author
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Vanhoenacker FM, Pelckmans MC, De Beuckeleer LH, Colpaert CG, and De Schepper AM
- Subjects
- Aged, Biopsy, Diagnosis, Differential, Female, Fingers pathology, Foot pathology, Graves Disease pathology, Humans, Myxedema pathology, Osteoarthropathy, Secondary Hypertrophic pathology, Skin pathology, Syndrome, Graves Disease diagnosis, Magnetic Resonance Imaging, Myxedema diagnosis, Osteoarthropathy, Secondary Hypertrophic diagnosis, Tomography, X-Ray Computed
- Abstract
Thyroid acropachy is a rare manifestation of autoimmune thyroid disease, in the form of soft tissue swelling of the hands and feet with insidious onset, associated with clubbing and characteristic periosteal reactions. It is usually part of a syndrome consisting of a typical triad of thyroid acropachy, exophthalmos, and pretibial myxedema. The purpose of this case report is to demonstrate the imaging features of this typical triad in a 65-year-old-woman. This case is the first in which the MRI features of thyroid dermopathy are documented.
- Published
- 2001
- Full Text
- View/download PDF
5. MR features of peripheral nerve sheath tumors: can a calculated index compete with radiologist's experience?
- Author
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Simoens WA, Wuyts FL, De Beuckeleer LH, Vandevenne JE, Bloem JL, and De Schepper AM
- Subjects
- Adolescent, Adult, Aged, Aged, 80 and over, Child, Child, Preschool, Diagnosis, Differential, Female, Humans, Infant, Male, Middle Aged, Observer Variation, Prospective Studies, Reproducibility of Results, Clinical Competence, Magnetic Resonance Imaging standards, Nerve Sheath Neoplasms diagnosis, Soft Tissue Neoplasms diagnosis
- Abstract
The aims of this study were, firstly, to provide a formula (neurogenic index) based on MR characteristics used in daily routine for predicting whether a soft tissue tumor is neurogenic or not, secondly, to test prospectively the performance of this formula, and thirdly, to compare this performance with that of radiologists experienced in MR imaging of soft tissue tumors. Retrospectively, MR images of 70 neurogenic and 70 non-neurogenic soft tissue tumors were evaluated in random order by two teams of two observers each. A neurogenic index (NI) was calculated based on those MR parameters that showed no or minor interobserver variability. Subsequently, three investigators in concert used the NI in a validation group of 15 neurogenic and 22 nonneurogenic soft tissue tumors. The same team, based on their own experience, tried to differentiate in the same validation group neurogenic from non-neurogenic soft tissue tumors. This was expressed in a subjective score (SS). Sensitivity, specificity, and predictive values were calculated. NI comprised spread (intra- or extracompartmental), distribution, fluid-fluid levels, homogeneity on T2-weighted images (WI), highest signal intensity (SI) on T1WI, lowest SI on T2WI, and delineation on T2WI. In the validation group, NI had a sensitivity of 88.6%, a specificity of 52.0%, a positive predictive value (PPV) of 54.1%, and a negative predictive value (NPV) of 84.6% for neurogenic tumors. The subjective score SS was superior and had a sensitivity of 93.3%, a specificity of 77.2%, a PPV of 73.7%, and a NPV of 94.4%. Our NI was less accurate than the SS; however, the low number of false-negative diagnoses for neurogenic tumors warrants continued efforts in development of neural networks.
- Published
- 2001
- Full Text
- View/download PDF
6. Metachronous eosinophilic granuloma of bone.
- Author
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Vanhoenacker FM, De Beuckeleer LH, De Roeck F, Mulier E, and De Schepper AM
- Subjects
- Bone Diseases diagnostic imaging, Child, Preschool, Eosinophilia diagnostic imaging, Female, Granuloma diagnostic imaging, Humans, Radiography, Bone Diseases complications, Eosinophilia complications, Granuloma complications
- Abstract
We present the case of a 4-year-old girl who developed a metachronous osseous lesion of the left distal femur five months after successful surgical treatment of an eosinophilic granuloma in the left proximal femur. After treatment of the second lesion with curettage, no further recurrence occurred during a follow-up interval of 17 months. Radiologists should be aware that additional eosinophilic granulomas of bone, occurring in up to four years after the initial diagnosis, should still be interpreted as a localized form of Langerhans'cell histiocytosis with a more favorable prognosis than the multifocal disseminated form, with involvement of organ systems other than the skeletal system.
- Published
- 2000
7. Images in clinical radiology. Bicipitoradial bursitis.
- Author
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Vanhoenacker FM, De Beuckeleer LH, and De Schepper AM
- Subjects
- Adult, Humans, Magnetic Resonance Imaging, Male, Radius pathology, Synovial Membrane pathology, Tendons pathology, Tomography, X-Ray Computed, Arm, Bursitis diagnosis, Muscle, Skeletal pathology
- Published
- 2000
8. MR imaging of clear cell sarcoma (malignant melanoma of the soft parts): a multicenter correlative MRI-pathology study of 21 cases and literature review.
- Author
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De Beuckeleer LH, De Schepper AM, Vandevenne JE, Bloem JL, Davies AM, Oudkerk M, Hauben E, Van Marck E, Somville J, Vanel D, Steinbach LS, Guinebretière JM, Hogendoorn PC, Mooi WJ, Verstraete K, Zaloudek C, and Jones H
- Subjects
- Adolescent, Adult, Aged, Diagnosis, Differential, Female, Humans, Immunohistochemistry, Male, Middle Aged, Retrospective Studies, Magnetic Resonance Imaging, Sarcoma, Clear Cell pathology, Soft Tissue Neoplasms pathology
- Abstract
Objective: To evaluate MR imaging and pathology findings in order to define the characteristic features of clear cell sarcoma of the soft tissues (malignant melanoma of the soft parts)., Design and Patients: MR examinations of 21 patients with histologically proven clear cell sarcoma of the musculoskeletal system were retrospectively reviewed and assessed for shape, homogeneity, delineation, signal intensities on T1- and T2-weighted images, contrast enhancement, relationship with adjacent fascia or tendon, secondary bone involvement, and intratumoral necrosis. In 19 cases the pathology findings were available for review and for a comparative MR-pathology study., Results: On T1-weighted images, lesions were isointense (n=3), hypointense (n=7) or slightly hyperintense to muscle (n=11). Immunohistochemical examination was performed in 17 patients. All 17 specimens showed positivity for HMB-45 antibody. In nine of 11 lesions with slightly increased signal intensity on T1-weighted images, a correlative MR imaging-pathology study was possible. All nine were positive to HMB-45 antibody., Conclusions: Clear cell sarcoma of the musculoskeletal system often has a benign-looking appearance on MR images. In up to 52% of patients, this lesion with melanocytic differentiation has slightly increased signal intensity on T1-weighted images compared with muscle. As the presence of this relative higher signal intensity on T1-weighted images is rather specific for tumors displaying melanocytic differentiation, radiologists should familiarize themselves with this rare entity and include it in their differential diagnosis when confronted with a well-defined, homogeneous, strongly enhancing mass with slightly higher signal intensity compared with muscle on native T1-weighted images.
- Published
- 2000
- Full Text
- View/download PDF
9. Desmoplastic fibroma of bone: MRI features.
- Author
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Vanhoenacker FM, Hauben E, De Beuckeleer LH, Willemen D, Van Marck E, and De Schepper AM
- Subjects
- Adult, Biopsy, Needle, Bone Neoplasms diagnostic imaging, Bone Neoplasms pathology, Diagnosis, Differential, Fibroma, Desmoplastic diagnostic imaging, Fibroma, Desmoplastic pathology, Humans, Knee diagnostic imaging, Knee pathology, Magnetic Resonance Imaging, Male, Tomography, X-Ray Computed, Bone Neoplasms diagnosis, Fibroma, Desmoplastic diagnosis
- Abstract
Desmoplastic fibroma of bone is a very rare benign tumor, which may be locally aggressive. In contrast to the well-documented radiological appearance, the literature on MR imaging features of this tumor is scarce. The MR imaging characteristics in our case are compared to those previously reported. Although there is a considerable overlap in the MR imaging features with other bone tumors, an interesting MR feature of desmoplastic fibroma is the presence of low to intermediate signal intensity foci on T2-weighted images, which radiographically does not correspond to calcifications. This feature may help narrow the differential diagnosis.
- Published
- 2000
- Full Text
- View/download PDF
10. Proteus syndrome: MRI characteristics of plantar cerebriform hyperplasia.
- Author
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Vanhoenacker FM, De Beuckeleer LH, Deprettere A, De Moor A, and De Schepper AM
- Subjects
- Child, Diagnosis, Differential, Foot diagnostic imaging, Humans, Hyperplasia, Male, Radiography, Foot pathology, Magnetic Resonance Imaging, Proteus Syndrome diagnosis
- Abstract
Proteus syndrome is a rare congenital hamartomatous syndrome with a variety of abnormalities. It shares many features with other congenital hamartomatous disorders, but cerebriform hyperplasia of the soles and the palms is known as a quite distinctive characteristic in the dermatologic literature. The purpose of this case report is to demonstrate the MRI features of plantar cerebriform hyperplasia in a 9-year-old boy with known Proteus syndrome.
- Published
- 2000
- Full Text
- View/download PDF
11. Sclerosing bone dysplasias: genetic and radioclinical features.
- Author
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Vanhoenacker FM, De Beuckeleer LH, Van Hul W, Balemans W, Tan GJ, Hill SC, and De Schepper AM
- Subjects
- Bone Diseases, Developmental classification, Bone Diseases, Developmental genetics, Bone Diseases, Developmental pathology, Humans, Radiography, Sclerosis, Bone Diseases, Developmental diagnostic imaging
- Abstract
Although knowledge of basic genetics in the field of sclerosing bone dysplasias is progressing, the radiologist still plays a pivotal role in the diagnosis of this relatively poorly understood group of disorders. Based on a target site approach, these anomalies are classified into three groups. Within each group, further differentiation can be made by distinctive clinical findings and by mode of inheritance: (a) dysplasias of endochondral bone formation: osteopetrosis (Albers-Schönberg disease), pycnodysostosis, enostosis, osteopoikilosis, osteopathia striata (Voorhoeve disease); (b) dysplasias of intramembranous bone formation: progressive diaphyseal dysplasia (Camurati-Engelmann disease) and variants, hyperostosis corticalis generalisata (Van Buchem disease) and variants; and (c) mixed sclerosing dysplasias: melorheostosis (Leri disease) and overlap syndromes.
- Published
- 2000
- Full Text
- View/download PDF
12. Imaging of Soft Tissue Tumors in the Pediatric Patient.
- Author
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Schepper AM, De Beuckeleer LH, and Vandevenne JE
- Abstract
The presence of a soft tissue mass in children is of concern to parents and physicians. Fortunately, these masses are rare and usually benign or pseudotumoral. When dealing with malignant soft tissue tumors, therapeutic options and long-term survival are strongly related to the disease stage at the time of diagnosis. Therefore, when children present with indeterminate or persisting symptoms and posttraumatic, metabolic, or infectious disorders have been ruled out, one should perform dedicated imaging studies (conventional radiography, computed tomography [CT], or both; sonography; magnetic resonance [MR] imaging) to exclude the possibility of a nonpalpable soft tissue mass or to characterize the mass when present. An overview of the use of the different imaging modalities for evaluating soft tissue tumors in the pediatric patient is presented. Because of the numerous benign, malignant, and pseudotumoral soft tissue masses that are often encountered in children, clinical, histologic, and imaging features are presented as concise tables.
- Published
- 1999
- Full Text
- View/download PDF
13. Magnetic resonance imaging of pelvic bone tumors.
- Author
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De Beuckeleer LH, De Schepper AM, and Ramon F
- Subjects
- Adolescent, Adult, Aged, Bone Neoplasms diagnostic imaging, Bone Neoplasms secondary, Child, Child, Preschool, Female, Humans, Male, Middle Aged, Pelvic Bones diagnostic imaging, Retrospective Studies, Tomography, X-Ray Computed, Bone Neoplasms pathology, Magnetic Resonance Imaging, Pelvic Bones pathology
- Abstract
The aim of our study was to determine the value of magnetic resonance (MR) imaging in the diagnostic workup of pelvic bone tumors. We retrospectively evaluated the MR findings in 60 pelvic bone tumors. Owing to its high contrast resolution and multiplanar imaging capabilities, MR offers a clear depiction of cortical, medullar or soft tissue involvement, intratumoral necrosis, and relationship to neurovascular structures, and may be considered as the modality of choice for the staging of pelvic bone tumors. Since grading of bone tumors reaches a high accuracy on conventional radiography (CR), the value of MR imaging is rather complementary. Although the role of MR imaging in tissue characterization is mostly limited to recognition of tumoral components, accurate tissue characterization if often possible (e.g. in low-grade chondrosarcoma, eosinophilic granuloma, aneurysmal bone cyst, giant cell tumor, and chordoma). MR imaging in osteochondromas, metastases, and fibrous dysplasia remains of limited value since most of these lesions are well recognized on CR and/or CT. CR remains the first choice examination in diagnosis and grading of bone tumors, but MR imaging has significantly improved staging and tissue characterization in bone tumor imaging. The aim of our study is to determine the value of magnetic resonance (MR) imaging in the diagnostic workup of pelvic bone tumors, i.e. in staging, in differentiating benign from malignant tumors (grading), and in further characterization of tumors or tumoral components.
- Published
- 1996
14. Magnetic resonance imaging of cartilaginous tumors: is it useful or necessary?
- Author
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De Beuckeleer LH, De Schepper AM, and Ramon F
- Subjects
- Adult, Bone Neoplasms diagnostic imaging, Chondroma diagnostic imaging, Chondrosarcoma diagnostic imaging, Female, Humans, Magnetic Resonance Imaging, Male, Osteochondroma diagnostic imaging, Radiography, Retrospective Studies, Bone Neoplasms diagnosis, Chondroma diagnosis, Chondrosarcoma diagnosis, Osteochondroma diagnosis
- Abstract
Objective: A retrospective study was undertaken to compare the diagnostic accuracy of plain radiography and magnetic resonance (MR) imaging in the diagnosis of cartilaginous tumors., Patients: The study population consisted of 68 patients with a histologically proven cartilaginous tumor., Design: For each lesion, a comparative analysis of "plain radiography" versus "plain radiography together with MR study" was performed by two radiologists together. Recently reported literature data were used as criteria by which to define accuracy rating., Results and Conclusions: MR imaging improves accuracy in diagnosing low-grade chondrosarcomas. Since osteochondromas have a characteristic appearance on plain films, MR imaging contributes only in the diagnostic workup of cases in which malignant transformation is suspected.
- Published
- 1996
- Full Text
- View/download PDF
15. Magnetic resonance imaging of pilomatricoma.
- Author
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De Beuckeleer LH, De Schepper AM, and Neetens I
- Subjects
- Contrast Media, Forearm, Gadolinium, Hair Diseases diagnostic imaging, Hair Diseases pathology, Humans, Image Enhancement, Infant, Male, Middle Aged, Pilomatrixoma diagnostic imaging, Pilomatrixoma pathology, Skin Neoplasms diagnostic imaging, Skin Neoplasms pathology, Ultrasonography, Hair Diseases diagnosis, Magnetic Resonance Imaging, Pilomatrixoma diagnosis, Skin Neoplasms diagnosis
- Abstract
Two patients (a 16-month-old boy and a 53-year-old man) were referred for MR imaging of a small, subcutaneous nodule at the forearm. Plain films were available in one patient and showed a non-specific well-circumscribed lesion. Upon ultrasonography (1 patient), a nodular, well-circumscribed, hyperechoic lesion was seen. In both cases spin-echo (SE) T1-weighted images (T1WI) showed homogeneous, intermediate signal intensity (SI). On gadolinium-enhanced T1WI (1 patient), no enhancement was observed. Both lesions showed predominant low-to-intermediate SI on T2WI. At histological examination characteristic findings of pilomatricoma were observed.
- Published
- 1996
- Full Text
- View/download PDF
16. Magnetic resonance imaging of cartilaginous tumors: a retrospective study of 79 patients.
- Author
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De Beuckeleer LH, De Schepper AM, Ramon F, and Somville J
- Subjects
- Adolescent, Adult, Aged, Aged, 80 and over, Bone Neoplasms classification, Bone and Bones pathology, Child, Child, Preschool, Chondroblastoma classification, Chondroma classification, Chondromatosis, Synovial classification, Chondrosarcoma classification, Diagnosis, Differential, Female, Humans, Infant, Male, Middle Aged, Retrospective Studies, Bone Neoplasms diagnosis, Chondroblastoma diagnosis, Chondroma diagnosis, Chondromatosis, Synovial diagnosis, Chondrosarcoma diagnosis, Magnetic Resonance Imaging methods
- Abstract
Objective: Hyaline cartilaginous tumors are characterized by extremely high signal intensity on T2-weighted images. Recently, some distinctive MR features of cartilaginous bone tumors were reported in small series. Low signal intensity septa surrounding high signal intensity cartilage lobules were seen on T2-weighted images in low-grade chondrosarcomas. On spin-echo T1-weighted images after Gd contrast injection, marked 'septal' or 'ring-and-arc' enhancement was observed in low-grade chondrosarcomas and enchondromas. The purpose of this study was to determine sensitivity and specificity of these MR findings in diagnosis of cartilaginous tumors, and to assess the value of MR in diagnostic workup of these lesions., Materials and Methods: Retrospective evaluation of MR findings in 79 cartilaginous tumors and in 79 non-cartilaginous tumors. All lesions were biopsy proven. Each MR examination was independently reviewed by two experienced radiologists without knowledge of clinical data, radiographic and/or CT findings, or histological diagnosis. All lesions were evaluated for morphology (lobular or non-lobular), presence of a high signal intensity mass on T2-weighted images, presence of low signal intensity septa separating high signal intensity lobules on T2-weighted images, and evidence of septal ('ring-and-arc') enhancement., Results: None of the reviewed parameters is useful in diagnosing osteochondromas. Since osteochondromas have a characteristic appearance on plain radiography, the value of MR imaging in the workup of these lesions remains limited. MR findings in enchondromas have a low specificity and a low sensitivity. Low-grade chondrosarcomas, often hard to diagnose on plain radiography and difficult to differentiate from enchondromas, are characterized by the MR tandem of 'low signal intensity septa on T2-weighted images' together with 'septal or ring-and-arc enhancement' (sensitivity 92.3%, specificity 76.5%). High-grade chondrosarcomas are easily recognized on plain radiography., Conclusions: In differentiating cartilaginous from non-cartilaginous tumors, MR features are highly specific but lack sensitivity. Grading potentials of MR parameters are promising due to the high accuracy in diagnosing low-grade chondrosarcomas.
- Published
- 1995
- Full Text
- View/download PDF
17. Chondrosarcoma in a patient with relapsing polychondritis.
- Author
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Fransen HR, Ramon FA, De Schepper AM, De Beuckeleer LH, Bal J, and Goovaerts G
- Subjects
- Bone Neoplasms diagnosis, Chondrosarcoma diagnosis, Diagnosis, Differential, Humans, Magnetic Resonance Imaging, Male, Middle Aged, Polychondritis, Relapsing diagnosis, Soft Tissue Neoplasms complications, Soft Tissue Neoplasms diagnosis, Tomography, X-Ray Computed, Bone Neoplasms complications, Chondrosarcoma complications, Polychondritis, Relapsing complications, Ribs
- Abstract
A case of a chondrosarcoma in a patient with relapsing polychondritis was presented. The association of these two unusual disorders of cartilaginous tissue has never been described before. The clinical presentation and radiologic and histologic features were discussed.
- Published
- 1995
- Full Text
- View/download PDF
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