1. P38.08: Dehydrated hereditary stomatocytosis showing variable expressivity: Report of two cases and review of the literature
- Author
-
A. Nguyen, L. Garçon, O. Ami, M. V. Senat, René Frydman, and Olivier Picone
- Subjects
medicine.medical_specialty ,Polyhydramnios ,Radiological and Ultrasound Technology ,business.industry ,medicine.medical_treatment ,Obstetrics and Gynecology ,General Medicine ,medicine.disease ,Pericardial effusion ,Surgery ,Benign tumor ,Reproductive Medicine ,Pericardiocentesis ,medicine ,Dehydrated hereditary stomatocytosis ,Radiology, Nuclear Medicine and imaging ,Immature teratoma ,Teratoma ,business ,Venous return curve - Abstract
ensuing weeks the mass increased in size, causing compression of venous return with increase in pericardial effusion, development of cariomegaly with A-V valves regurgitation, polyhydramnios, and ascites. Pericardiocentesis was performed. By 34 wks the mass had grown to 43 × 44 mm with worsening cardiac failure; the baby was delivered by C/S followed by neonatal cardiac surgery (Fig 1b), but the baby died on the 5th day of life. Pathology analysis of tumor tissue showed invasive immature teratoma (Fig 1b-c). Discussion: Pericardial teratoma is generally a benign tumor, with good outcome after neonatal cardiac surgery. In this case the fastgrowing tumor proved to be a lethal invasive immature teratoma.
- Published
- 2008