1. Primary pancreatic cystic neoplasms of the pancreas revisited. Part IV: rare cystic neoplasms.
- Author
-
Sakorafas GH, Smyrniotis V, Reid-Lombardo KM, and Sarr MG
- Subjects
- Adult, Carcinoma, Pancreatic Ductal surgery, Choriocarcinoma pathology, Choriocarcinoma surgery, Female, Hamartoma pathology, Hamartoma surgery, Hemangioma, Cavernous pathology, Hemangioma, Cavernous surgery, Humans, Lymphangioma, Cystic pathology, Lymphangioma, Cystic surgery, Male, Middle Aged, Pancreatic Cyst surgery, Pancreatic Neoplasms surgery, Rare Diseases pathology, Rare Diseases surgery, Teratoma pathology, Teratoma surgery, Tomography, X-Ray Computed, Pancreatic Neoplasms, Carcinoma, Pancreatic Ductal pathology, Pancreatic Cyst pathology, Pancreatic Neoplasms pathology
- Abstract
Primary pancreatic cystic neoplasms are being recognized with increasing frequency due to modern imaging techniques. In addition to the more common cystic neoplasms-serous cystadenoma, primary mucinous cystic neoplasm, and intraductal papillary mucinous neoplasm-there are many other less common neoplasms that appear as cystic lesions. These cystic neoplasms include solid pseudopapillary neoplasm of the pancreas (the most common rare cystic neoplasm), cystic neuroendocrine neoplasm, cystic degeneration of otherwise solid neoplasms, and then the exceedingly rare cystic acinar cell neoplasm, intraductal tubular neoplasm, angiomatous neoplasm, lymphoepithelial cysts (not true neoplasms), and few others of mesenchymal origin. While quite rare, the pancreatic surgeon should at the least consider these unusual neoplasms in the differential diagnosis of potentially benign or malignant cystic lesions of the pancreas. Moreover, each of these unusual neoplasms has their own natural history/tumor biology and may require a different level of operative aggressiveness to obtain the optimal outcome., (Copyright © 2011 Elsevier Ltd. All rights reserved.)
- Published
- 2012
- Full Text
- View/download PDF