1. Type I split cord malformation and tethered cord syndrome in an adult patient: A case report and literature review
- Author
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Vyacheslav Makler, Erin D’Agostino, John H. Kanter, Imad Saeed Khan, David F Bauer, and Daniel R. Calnan
- Subjects
Adult ,medicine.medical_specialty ,Split cord ,Cord ,medicine.medical_treatment ,Case Report ,030218 nuclear medicine & medical imaging ,03 medical and health sciences ,Spina bifida occulta ,Diastematomyelia ,0302 clinical medicine ,Lumbar ,medicine ,Tethered Cord ,Tethered cord ,medicine.diagnostic_test ,business.industry ,fungi ,Laminectomy ,Magnetic resonance imaging ,medicine.disease ,Spinal cord ,Surgery ,medicine.anatomical_structure ,Neurology (clinical) ,business ,030217 neurology & neurosurgery - Abstract
Background: In a split cord malformation (SCM), the spinal cord is divided longitudinally into two distinct hemicords that later rejoin. This can result in a tethered cord syndrome (TCS). Rarely, TCS secondary to SCM presents in adulthood. Here, we present an adult female with Type I SCM resulting in TCS and a review of literature. Case Description: A 57-year-old female with a history of spina bifida occulta presented with a 2-year history of worsening back and left leg pain, difficulty with ambulation, and intermittent urinary incontinence; she had not responded to conservative therapy. Magnetic resonance imaging (MRI) revealed a tethered cord secondary to lumbar type I SCM. The patient underwent an L1–S1 laminectomy for resection of the bony septum with cord detethering. At 2-month follow-up, the patient had improvement in her motor symptoms and less pain. In literature, 25 cases of adult-onset surgically managed SCM with TCS were identified (between 1936 and 2018). Patients averaged 37 years of age at the time of diagnosis, and 56% were female. Conclusion: TCS can present secondary to SCM in adulthood and is characterized predominantly by back and leg pain.
- Published
- 2019