1. Retroperitoneal Sclerosing Lipogranuloma in an Adolescent With Congenital Atresia of the Inferior Vena Cava: Case Report and Literature Review
- Author
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Abdur Rauf Khan, Phillip Benson Ham, Abdulraouf Lamoshi, David H. Rothstein, Pierre Williot, Beverly Schaefer, Richard Cheney, and Clare Twist
- Subjects
medicine.medical_specialty ,Adolescent ,Subcutaneous Fat ,Vena Cava, Inferior ,Lipidoses ,Inferior vena cava ,03 medical and health sciences ,Congenital atresia ,0302 clinical medicine ,medicine ,Back pain ,Humans ,Inflammation ,Venous Thrombosis ,Retroperitoneal mass ,business.industry ,Retroperitoneal Fibrosis ,Hematology ,Sclerosing lipogranuloma ,medicine.disease ,Venous thrombosis ,Oncology ,medicine.vein ,030220 oncology & carcinogenesis ,Atresia ,Pediatrics, Perinatology and Child Health ,cardiovascular system ,Etiology ,Female ,Radiology ,medicine.symptom ,business ,030215 immunology - Abstract
Sclerosing lipogranuloma (SLG) in children is a rare, benign disease of unknown etiology suspected to be due to abnormal fatty tissue reaction. A 13-year-old girl presented with progressively worsening back pain. Cross-sectional imaging identified a retroperitoneal mass compressing the left ureter as well as infrarenal inferior vena cava atresia with extensive venous collaterals and chronic partially occlusive thromboses of the iliac veins. Surgical biopsy was consistent with SLG and it resolved spontaneously. SLG is typically a disease of adulthood but may be seen in children. The association between inferior vena cava atresia with venous thrombosis and development of SLG has not been reported previously.
- Published
- 2020
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