Search

Your search keyword '"Porphyria, Hepatoerythropoietic complications"' showing total 3 results
Start Over Descriptor "Porphyria, Hepatoerythropoietic complications" Journal journal of hepatology
3 results on '"Porphyria, Hepatoerythropoietic complications"'

3. Liver transplantation for erythropoietic protoporphyria. Report of a new case with subsequent medium-term follow-up.

Author

Mion FB, Faure JL, Berger F, McGregor B, Perrot H, and Paliard P

Subjects
Adult, Dermatitis, Photoallergic etiology, Follow-Up Studies, Humans, Liver metabolism, Male, Porphyria, Hepatoerythropoietic complications, Porphyria, Hepatoerythropoietic metabolism, Protoporphyrins biosynthesis, Recurrence, Liver Transplantation, Porphyria, Hepatoerythropoietic surgery
Abstract

We report a new case of successful liver transplantation in a 36-year-old patient with terminal hepatic failure due to erythropoietic protoporphyria. Data regarding protoporphyrin levels in erythrocytes and feces, before and after transplantation, seem to indicate that in this case protoporphyrin overproduction was in part due to liver synthesis. Four years after surgery, the patient is completely free of skin photosensitivity. His liver function tests are normal; there are no visible protoporphyrin deposits or ultrastructural abnormalities in his new liver. However, recurrence of the disease in the long term cannot be excluded, since erythrocyte protoporphyrin levels remained elevated after liver transplantation.

Published
1992
Full Text
View/download PDF

Catalog

Books, media, physical & digital resources
See catalog results