1. Systemic capillary leak syndrome
- Author
-
Hiroshi Arima, Soichi Sugahara, Hidetomo Nakamoto, Kenshi Moriwaki, Hirokazu Okada, Ruri Chihara, Yoshihiko Kanno, and Hiromichi Suzuki
- Subjects
Male ,medicine.medical_specialty ,business.industry ,General Medicine ,Middle Aged ,Pulmonary edema ,medicine.disease ,Surgery ,Hypoproteinemia ,Shock (circulatory) ,Anesthesia ,Edema ,Intensive care ,Internal Medicine ,medicine ,Systemic capillary leak syndrome ,Humans ,Hypoalbuminemia ,medicine.symptom ,business ,Capillary Leak Syndrome - Abstract
Systemic capillary leak syndrome (SCLS) is characterized by recurrent hypovolemic shock attributable to increased systemic capillary leakage. A 46-year-old man was admitted to our hospital because of recurrent episodes of generalized edema with hypovolemic shock. Blood laboratory data revealed severe hypoproteinemia with a small monoclonal IgG-kappa protein. These findings suggested strongly the diagnosis of SCLS. A regimen with steroid pulse therapy was tried; however, intravascular overloading accompanied by the recruitment of the initially extravasated fluids resulted in acute pulmonary edema. Intensive care and careful monitoring of fluid volume are required in SCLS.
- Published
- 2002