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Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a genetically determined cardiomyopathy characterized by fibrofatty replacement of predominantly, right ventricular (RV) myocardium.1 Morphologic changes frequently occur at the inferior-subtricuspid and mid RV outflow (RVOT), and may involve the antero-apical region in severe cases (triangle of dysplasia).2 As disease progresses, global RV dilation and RV dysfunction may occur. RV structural changes may also lead to development of functional tricuspid regurgitation (TR), often in the absence of pressure overload from the pulmonary vasculature (e.g. pulmonary hypertension or left heart failure). Therefore, TR in the context of ARVD/C may represent a unique phenotype of patients with functional TR. Because RV volume overload from significant TR may in turn worsen RV function, surgical correction of TR could have therapeutic benefit. Both significant TR and RV dysfunction have been independently associated with worse prognosis in ARVD/C.3-4 In order to better understand the potential role of surgery in these patients, we reviewed our ARVD/C database to identify patients who underwent surgical correction of TR.