1. Clinical recognition of mid-aortic syndrome in children
- Author
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Roel L. F. van der Palen, Kim ten Dam, Michiel F. Schreuder, Ronald B. Tanke, Huib de Jong, and Paediatric Cardiology
- Subjects
Male ,medicine.medical_specialty ,Health aging / healthy living [IGMD 5] ,Adolescent ,Vascular Malformations ,Aortic Diseases ,Physical examination ,Disease ,Vascular anomaly ,Fatal Outcome ,Hydrops fetalis ,medicine.artery ,Internal medicine ,medicine ,ABDOMINAL BRUIT ,Humans ,Aorta, Abdominal ,Child ,Renal disorder [IGMD 9] ,Aorta ,medicine.diagnostic_test ,business.industry ,Abdominal aorta ,Infant, Newborn ,Functional imaging [IGMD 1] ,Syndrome ,medicine.disease ,Surgery ,Blood pressure ,Child, Preschool ,Hypertension ,Pediatrics, Perinatology and Child Health ,Cardiology ,Female ,business - Abstract
Item does not contain fulltext Mid-aortic syndrome is characterized by narrowing of the abdominal aorta, usually with the involvement of renal arteries and other visceral branches. The combination of the presence of an abdominal bruit, diminished or absent pulsations of the lower extremities, and a blood pressure discrepancy between upper and lower extremities is the classic triad associated with mid-aortic syndrome. However, it has a wide variety of clinical symptoms, and awareness of the variable presentation can lead to early diagnosis of the vascular anomaly. We report three cases presenting at three different stages of this disease, such as hydrops fetalis, refractory hypertension, and intracerebral bleeding. In conclusion, these cases highlight the importance of blood pressure measurements in all patients and accurate physical examination for early recognition of a mid-aortic syndrome. 01 maart 2013
- Published
- 2013