1. Pulmonary Hamartoma Syndrome
- Author
-
Barbara Y. Zara and Nashat Y. Gabrail
- Subjects
Adult ,Male ,Pulmonary and Respiratory Medicine ,congenital, hereditary, and neonatal diseases and abnormalities ,Pathology ,medicine.medical_specialty ,Lung Neoplasms ,Adolescent ,Hamartoma ,Critical Care and Intensive Care Medicine ,Clinical investigation ,medicine ,Humans ,In patient ,Aged ,Aged, 80 and over ,business.industry ,Respiratory disease ,Syndrome ,Middle Aged ,medicine.disease ,Pulmonary Hamartoma ,stomatognathic diseases ,embryonic structures ,Female ,Congenital disease ,business ,Cardiology and Cardiovascular Medicine - Abstract
We reviewed 24 charts of patients with pulmonary hamartoma; numerous congenital anomalies and benign tumors were observed in this series. Most of the observed associations are known to occur in patients with Cowden's syndrome, which is characterized by multiple hamartomatous neoplasms of ectodermal, mesodermal, and endodermal origin; however, to our knowledge, there has been no reported association between pulmonary hamartoma and Cowden's syndrome. We conclude that pulmonary hamartomas are frequently accompanied by other developmental abnormalities and benign tumors.
- Published
- 1992