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Your search keyword '"O, Bitterman-Deutsch"' showing total 2 results
Start Over Author "O, Bitterman-Deutsch" Journal british journal of dermatology
2 results on '"O, Bitterman-Deutsch"'

1. Mal de Meleda keratoderma with pseudoainhum

Author

Reuven Bergman, Rachel Friedman-Birnbaum, R Gershoni-Baruch, Manigé Fartasch, and O. Bitterman-Deutsch

Subjects
congenital, hereditary, and neonatal diseases and abnormalities, medicine.medical_specialty, Keratosis, Hyperkeratosis, Etretinate, Hand Dermatoses, Dermatology, Ainhum, Hand Dermatosis, medicine, Humans, Child, skin and connective tissue diseases, Keratoderma, Skin, Foot Dermatoses, business.industry, medicine.disease, Dyskeratosis, Pedigree, Surgery, Microscopy, Electron, Family member, Female, business, medicine.drug
Abstract

Pseudoainhum is an infrequent complication in the autosomal-recessive keratodermas. We describe two related families in which the diagnosis of mal de Meleda keratoderma has been confirmed by mode of inheritance and ultrastructural findings. One family member, a 9-year-old girl, developed pseudoainhum which threatened the viability of her little fingers. This responded to treatment with etretinate. The treatment dilemma posed by keratoderma-induced pseudoainhum in children, i.e. the concern over the possible skeletal toxic effects of long-term etretinate treatment vs. the risks and outcome of surgery, is discussed.

Published
1993

2. Mal de Meleda keratoderma with pseudoainhum.

Author

Bergman R, Bitterman-Deutsch O, Fartasch M, Gershoni-Baruch R, and Friedman-Birnbaum R

Subjects
Ainhum drug therapy, Child, Etretinate therapeutic use, Female, Foot Dermatoses genetics, Foot Dermatoses pathology, Hand Dermatoses genetics, Hand Dermatoses pathology, Humans, Keratosis genetics, Keratosis pathology, Microscopy, Electron, Pedigree, Skin ultrastructure, Ainhum etiology, Foot Dermatoses complications, Hand Dermatoses complications, Keratosis complications
Abstract

Pseudoainhum is an infrequent complication in the autosomal-recessive keratodermas. We describe two related families in which the diagnosis of mal de Meleda keratoderma has been confirmed by mode of inheritance and ultrastructural findings. One family member, a 9-year-old girl, developed pseudoainhum which threatened the viability of her little fingers. This responded to treatment with etretinate. The treatment dilemma posed by keratoderma-induced pseudoainhum in children, i.e. the concern over the possible skeletal toxic effects of long-term etretinate treatment vs. the risks and outcome of surgery, is discussed.

Published
1993
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